Thalasemia Konseling DR Indra

 

]gi`issfaei MEIDBL_E_, CLB_F@EBD MIB ]EBMIC @IBJV]

Ebmri Tejiyi Mevese Gfaitl`lde Lbcl`lde Afmec ‟ _AH. E`au [fbyicet Mi`ia ^_G_ >;>9 Nibmubd

 

]i`isfaei

MEIDBL_E_, CLB_F@EBD MIB ]EBMIC @IBJV]

]lpec pfanigisib     

Dianirib uaua ]i`isfaei Meidblses ]i`isfaei [fbdlnitib ]i`isfaei Ispfc [fbofdigib mib Clbsf`ebd _eapu`ib

 

 

 Ipicig tgi`issfaei etu< Cf`iebib mirig yibd metibmie mfbdib dibdduib  pfanfbtucib prltfeb (d`lneb) mebmebd sf` mirig afrig (fretrlset)

_f` mirig afrig afbjime aumig  pfoig

Ibfaei

AFBUFNINCIB IBFAEI (^EBDIB, _FMIBD, NF^I])

 

Gi` yd tfrjime pimi pisefb tgi`issfaei< Nf`ua imi  pfbdlnitib  pfbdlniti b yibd fhfcteh 

]^IB_HV_E ^V]EB

Dibdduib [fanfbtucib Mib [fbdgibourib _f` mirig afrig

IBFAEI

[FBVA[VCIB ZI] NF_E

DIBDDVIB HVBD_E L^DIB ]VNVG

Cfsicetib mib Cfaiteib

 

_pfctrua C`ebes [itldfbfses

 

Dfji`i c`ebes mib `inlritlreua

 Ibi`eses dfb: MBI (Ἃ, Ẓ)

 



Dibdduib sebtfses d`lneb 



[fanfbtucib fretrlset inblrai` 



Gfal`eses  



[fbuapucib zit nfse  



Autise itiu mf`fse dfb



 F`fctrlhlrf F`fctrlhlrfses ses gn  Dianirib fretrlset: ibseplece`lsetlses ibseplece`lsetlses  Ibfaei, Ectfrec   Gfpitl (sp`fblafdi`e) mib gfalogrlaitlses, gfalogrlaitlse s, gfalsemfrlses

 

_pfctrua c`ebes pfbmfreti tgi`issfaei nfrnfmi-nfmi

 

JFBE_-JFBE_ ]GI@I__FAEI 

Nfrmisircib Dfb yibd tfrdibddu: • ]gi`issfaei I`hi (ι) • ]gi`issfaei Nftgi (ξ)



Nfrmisircib Mfrijit Cfrusicib Dfb: • ]gi`issfaei (ι/ξ) aijlr  • ]gi`issfaei (ι/ξ) ebtfrafmeitf • ]gi`issfaei (ι/ξ) aeblr 



Nfrmisircib cfnutugib tribshuse: • ]gi`isfaei tribshuse ruteb (]>^), ]M] (]ribshuselb mfpfbmfbt tgi`issfaei): ibfaei nfrit, afafr`ucib tribshuse sfuaur gemup ubtuc tftip gemup. • ]gi`isfaei tribshuse temic ruteb (]?^), B]M] (Blb ]ribshuselb mfpfbmfbt tgi`issfaei): ibfaei rebdib/sfmibd, afafr`ucib tribshuse mi`ia clbmese-clbmese tfrtfbtu siji (temic rfdu`fr). ]igfr ft i`. @iboft >;973 ?59: 966‟84 

 

? Jfbes ]gi`isfaei 9

]I@I_FAEI AIUL^  • Meturubcib mire cfmui lribd tui (enu mib iyig) • Dfji`i sfmibd gebddi nfrit,  neisibyi aubou` siit niye  nfrusei 8 nu`ib. • Nutug tribshuse mirig yibd ruteb

>

]I@I_FAEI EB]F^AFMEI • ]ebdcit cfpirigib nfrimi me  pfrtfbdigib ibtiri ti`isfaei aiylr mib aeblr. • Afafr`ucib tribshuse mirig, biaub temic ruteb

?

]I@I_FAE I@I_FAEI I AEBL^  • Meturubcib gibyi mire 9 lribd tui (enu siji itiu iyig siji) • Neisibyi afae`ece dfji`i yibd rebdib / temic afae`ece dfji`i • ]emic nutug tribshuse mirig

 

Nidieaibi Meidblses ]i`isfaei metfdiccib<

Meidblses ]i`isfaei

 

Meidblses C`ebes Ibiabfses. • Cgis: puoit crlbec itiu  nfr`ibdsubd  nfr`ibdsub d `iai3 usei iwetib iwetib tfrjimebyi puoit pfbtebd ubtuc meidblses • ^ewiyit tribshuse nfru`ibd • ^ewiyit cf`uirdi mfbdib ]i`isfaei mib tribshuse nfru`ibd • ^ewiyit tuanug cfanibd mib  punfrtis tfr`ianit tfr`ianit

[fafrecsiib Hesec. • • • • • • •

[uoit3 clbjubdtevi ibfaes _c`fri ectfrec Hioefs Oll`fy Gfpitlsp`fblafdi`e, Didi` tuanug, pfriwicib pfbmfc  [unfrtis tfr`ianit Gepfrpedafbtise Gepfrpedafb tise cu`et.

Meidblses MBI/Dfbfteci

Meidblses @inlritlreua Mirig pfrehfr `fbdcip (M[@)

•

[l`yafrisf Ogieb ^fiotelb ([O^),

•

^fstreotelb Hridafbt @fbdtg [l`yalrpgesa (^H@[). Iap`eheoitelb ^fhriotlry Autitelb _oibbebd (I^A_).

• Ibfaei •  Be`ie AOX mib AOG yibd yibd rfbmig. • ^MT

Dianirib mirig tfpe. Ibeslsetlses, plece`lsetlses, hridafbtlset mib tfir-mrlp), aecrlsetec geplcrla,  nislpge`eo stepp`ebd, stepp`ebd, nimib nimib [ippfbgfeafr, [ippfbgfeafr, sf` tirdft

[iriaftfr nfse Hfreteb

F`fctrlhlrfses Gn Inblrai`etis GnH, Gn I

•

]ibmi mib mib Dfji`i Dfji`i ]i`isfaei ]i`isfaei

 

Ibfaei Dfji`i yibd pi`ebd sfrebd metfaucib Cf`ugib `faig, `fsu, cf`f`igib, puoit.

Aubdceb afbdi`iae: • • • •

Cu`et mib nideib puteg nl`i aiti afbdubebd Cf`f`igib pirig _icet mimi [frtuanugib ofbmfrubd `ianit

• Oioit wijig itiu cf`iebib tu`ibd, cgususbyi pimi nfbtuc • Ibfaei nfrit • _fsic bipis • [fanfsirib itiu nfbdcic me nideib pfrut • Vrebf nfrwirbi df`ip •  Bihsu aicib afburub afburub

Hioefs Oll`fy: Mige afblbjl`, aiti afbyepet, jiric cfmui aiti af`fnir,, aicse`i gepfrtrlhe, ai`lc`use dede. af`fnir

]ibmi mib mib Dfji`i Dfji`i ]i`isfaei ]i`isfaei

 

]ibmi mib dfji`i tfrdibtubd:        

Jfbes tgi`issfaei. Cimir zit nfse tunug (hfrreteb). Vsei. Nibyicbyi tribshuse yibd menfrecib. Dibdduib lrdib. Cfpitugib aebua lnit cf`ise nfse.

 

Dianirib _f` Mirig Afrig

 

FXI@VI_E GFAI]L@LDE ]I@I_FAEI 



Gn, Gfald`lneb ^NO, ^fm N`llm Of``  ^MT, rfm of`` mestrenulb wemtg AOX, afib olrpusou`ir vl`uaf ^ft, ^fou`loytf olubt ^ft-Gf TNO, `fuoloytf [@], p`itf`ft



Erlb

 

]ENO Hfrretb Ne`eruneb Ollan―s tfsts Gn f`fotrlpglr f`fotrlpglrfses fses G[@O

     

   

 Ipus mirig tfpe: Fretrlset: dianirib geplcrla aecrlsetfr, ibeslplece`lselses  (f`eptlset, nurr of``, sf` tirdft, tfir mrlps, spgfrloytf).

 

F@FC] ^LHL ^F_E _ G N [IMI [IMI ]I@I_ ]I@I_ FAEI  Gfald`lneb (%)

Cf`iebib

I

I>

H

5; ‟ 56

?,6 ‟ 4,;

9‟6

7; ‟ 56

9,; ‟ ?,6

6 ‟ >;

9; ‟ 5; ;

9,6 ‟ =,; 9,6 -=,;

9; ‟ 5; 57

8;-76

9,; ‟ >,;

96-?6

]i`isfaei  aeblr ]i`isfaei   aeblr ]i`isfaei  aiylr    

-  tgi` + -  tgi` ;

G[HG

G[HG 1 gfrfmetiry pfrsestfbof lh hfti` gifald`lnebs

 

O L B H E ^ A I] I] E L B L H I ] G I @ I _ _ I F A E I M E I D B L _ E _ TE]G GN F@FO]^L[GL^F_E_

Blrai` pifrb Blrai`  pifrb lh

F`fvifm GnI> eb

_glws GnG nibm eb

Gn f`forlpglrfses.

nfi gi`issfaei rie

i`pgi i`pgi gi`issfaei.  gi`issfaei.

 

O L B H E ^ A I] I] E L B L H I ] G I @ I _ _ I F A E I M E I D B L _ E _ T E ] G M B I I B I @U @U _ E _

 

Cipib mepfr`ucib ibi`eses MBI ubtuc meidblses tgi`issfaei

9. Meidb eidbls lses es [rfbiti` iti` >. Jeci Jeci gise` gise` pfafre pfafrecsi csiib ib ebmf ebmfcs cs sf` sf` mirig mirig afrig afrig mib mib ibi`ese ibi`esess Gn :  ‟ ]emic mipit afbfdiccib meidblses

 ‟ ]emic sfsuie mfbdib aibehfstise c`ebes ?. ]gi`is i`issf sfae aei i i`p i`pg gi:

 ‟ ]emic sfaui jfbes tgi`issfaei i`pgi mipit memeidblses mfbdib  pfafrecsiib gfaitl`lde =. ]gi`issfaei nf nfti: Vauabyi temic afafr`ucib ibi`eses MBI

 

[fr`ubyi Clbsf`ebd [imi [fbibdibib ]i`isfaei

 

CLB_F@EBD BD ]I@I_FAE ]I@I_FAEI I CLB_F@E

•

•

Clbsf`ebd ]i`isfaei ]i`isfaei imi`ig  prlsfs fmucise mib pfaigiaib cfpimi ebmevemu niec ebmevemu yibd sfgit, cirefr ] ]i`isfaei, i`isfaei, aiupub pfbyibmibd ] ]i`isfaei i`isfaei afbdfbie clbmese tunugbyi. Afae`ece pfrnfmiib mi`ia hlcus cijeib mib pfbfcibib sumut pibmibd.

 

CLB_F@EBD BD ]I@I_FAE ]I@I_FAEI I CLB_F@E CLB_F@EBD [IMI [FBUIBMIBD ]I@I_FAEI

CLB_F@EBD CF@VI^DI/AI_UI^ICI]

• [faigiaib tfbtibd ]i`isfaei sfoiri uaua. Nidieaibi pl`i

• [faigiaib judi meirigcib cfpimi sfaibdit gemup,

• [faigiaib tfbtibd ]i`isfaei sfoiri uaua.

 pfwiresib sehit itiu itiu cirefr cirefr.. • [faigiaib judi meirigcib cfpimi sfaibdit gemup,  nfrictevetis blrai`, blrai`, tuanug m mib ib  nfrcfanibd  nfrcfanib d sfnidieaib sfnidieaibii `iyicbyi ibic/ebmevemu `iebbyi. • [fbibdibib yibd ruteb mib tfritur afbjiaeb pfrcfanibdib hesec mib afbti` yibd lpteai`.

 nfrictevetis blrai`, blrai`, tuanug mib nfrcfanibd sfnidieaibi `iyicbyi ibic/ebmevemu ibic/ebmevem u `iebbyi. • [fbibdibib yibd ruteb mib tfritur afbjiaeb  pfrcfanibdib  pfrcfanib dib hesec mib afbti` yibd lpteai`. • Mespfbsise nide ci`ibdib  pfbyibmibd  pfbyibmib d mi`ia gi` tfrip tfripee tribshuse

Nidieaibi pl`i  pfwiresib sehit sehit itiu cirefr. • Nidieaibi nfrsecip mfbdib pfbyibmibd ]i`isfaei. • [fae`egib pisibdib becig, pfr`ubyi screbebd.

CLB_F@EBD [IMI EBMEXEMV BL^AI@

 

Afbdipi ]gi`isfaei Mipit Meofdig<

 

^fboibi ]ebmic @ibjut <

 

Afbdipi tgi`issfaei pfbtebd<

• Nf`ua mipit mesfanugcib (citistrlhec) • [fbyicet yd mipit meofdig.

• Afbyfnincib cui`etis gemup afburub. • Nfrmiapic psecl-slsei` mib fclblae  nide pisefb.

• Afanutugcib neiyi nfsir mi`ia pfbdlnitib. • Miapic slsei` fclblae nide

• Afbyfnincib nibyic clbmese pfbyicet ecutib (alrnemetis). (alrnemetis). • Afbebdcitcib cfaiteib (alrti`etis) usei aumi.

cf`uirdi. • Nfrmiapic fclblae nide bfdiri/isuribse.

Tlr`m Gfi`tg Lrdibezilb (TGL)

 

 

 

Hicti ]gi`issfaei • >4; juti lribd me MVBEI imi`ig MVBEI imi`ig pfbmfreti tgi`issfaei. • 8 ‟ 9; lribd Ebmlbfsei imi`ig pfaniwi pfaniwi sehit tgi`issfaei. • ]froitit 9;.696 pisefb pfbmfreti tgi`issfaei me EBMLBF_EI EBMLBF_EI.. • =.955 pfbmfreti (?5.5%) nfrisi` mire JITI NI^I] NI^I].. • Mfbdib jua`ig pfbmumuc sfcetir =5,5= juti jewi mib ibdci cf`igerib >;%, 8;;-9.;;; aici mepfrcericib icibtigubbyi `iger niye. tgi`issfaei sfnibyic lribd sfteip

Tlr`m Gfit`g Lrdibezilb (TGL) Tlr`m Gfit`g Lrdibezilb Lrdibezilb (TGL) >;97, [L[]E Jinir >;97

 

[FBOFDIGIB ]GI@I_FAEI

Vpiyi [fbofdigib ]gi`issfaei:

[rldria pfbofdigib: -

-

Afrupicib upiyi yibd  prictes.

-

Mipit me`icucib.

-

Afbjiwin sfaui pfrtibyiib mire pfraisi`igib ibic, cf`uirdi aiupub bfdiri.

-

-

-

-

Fmucise aisyiricit. _crebebd pfaniwi sehit (cirefr) mib screbebd aissi`. Clbsu`tise dfbftec pimi lribd  pfaniwi sehit. Meidblses prfbiti` (sfnf`ua cf`igerib) Inlrse pimi cfgiae`ib yibd  plseteh tgi`isfaei< tgi`isfaei<

]irdft plpu`ise: -

-

Aisyiricit uaua Cf`laplc resecl tebdde (rebd situ) Cf`laplc pribecig. Cf`laplc niru afbecig. Tibeti giae`.

 

_C^EBEBD vfrsus vfrsus MF]FC_E  MF]FC_E MEBE

_C^EBEBD • Afbdftigue meidblses `fneg iwi` mfbdib af`icucib pfafrecsiib (sfmfrgibi). • Vauabyi me`icucib pimi lribd yibd ‐sfgit‑.

MF]FC_E MEBE • Afbdftigue meidblses pfbyicet `fneg iwi` mfbdib afbdfbi` dfji`i mib tibmi mib sf`ibjutbyi af`icucib  pfafrecsiib-pfafrecsiib  pfafrecsiib-pf afrecsiib yi yibd bd tfpit. • Me`icucib pimi lribd yibd afapubyie resecl tebdde itiu meouredie tf`ig sicet sicet

 

Mftfcse mebe tgi`issfaei 9. Af Afbf bfdi dicc ccib ib m mei eidb dbls lses es IBFAEI!!! >. Af`icucib _C^EBEBD CF@VI^DI   CF@VI^DI  pfbyibmibd tgi`issfaei

 

MF]FC_E CI^EF^ ]GI@I_FAEI

Ibiabfses

[gyseoi` Fxia

_orffbebd @in

]gi`issfaei, temic nfrirte sf`i`u afafr`ucib tribshu tribshuse se mirig

Gn f`forlpglrfses ¹ MBI ibi`yses

 

 Ipicig _crebebd Afapubyie Miapic Afbdubtubdcib Vbtuc ]iti`icsibi ]gi`issfaei< Ui, sumig nibyic pfbf`eteib afanuctecib  nigwi upiyi pfbofdigib tgi`issfaei tgi`issfaei (mfbdib afbofdig afbofdig `igerbyi sflribd niye tgi`issfaei) afrupicib upiyi yibd olstfhhfotevf.

 

AFBOFDIG vfrsus AFBDLNI AFBDLNI]E ]E NEIUI [FBOFDIGIB

NEIUI ]I]I@IC_IBI

• • •

• • • •

_crebebd mirig Clbsf`ebd dfbftci _crebebd prfairei`

]ribshuse ]ribshuse mirig Lni cf`ise ]ii`icsibi clap`ecise @ieb-`ieb (lbdcls, m``)

Jiwi Niri ?.8?8 pisefb

¹ ^p 9,6 re`eub/i re`eub/igub gub

Ebmlbfsei ¹ 5.;;; pisefb

¹ EM^ ?,8 ¹ ^p ?;;.;;; -=;;.;;;/

lribd  

¹ ^p =;;.;;;.;;;/ lribd/tigub

9;;; x `epit Neiyi aibmere

Neiyi pfafrebtig

re`eub/igub −

 

 [rfbiti` Meidblses Meidblses

•

•

[fafrecsiib crlalsla (MBI)  jibeb Mfbdib afbddubicib  pibmuib V_D

Oglrelbeo ve``lus siap`ebd (OX_): cfgiae`ib 5-99 aebddu.

Iabelofbtfses itiu olrmlofbtfses: olrmlofbtfses: cfgiae`ib 97-95 aebddu.

 

 [rfbiti` Meidblses Meidblses

•

_faui pisibdib nfresecl pfr`u menfre clbsf`ebd tfbtibd meidblses prfbiti` ubtuc afaistecib stitus ti`isfaei jibeb.

•

Jeci jibeb bfditeh tgi`isfaei, cfgiae`ib mipit me`ibjutcib.

•

Jeci jibeb plsetep tgi`isfaei, pe`egib ubtuc afbdicgere cfgiae`ib metiwircib.

   

_li` #? _EI[I[VB…

_ftf`ig nfrlnit mib mepfrecsi me ^_G_ wibeti tfrsfnut afbmfreti  nesi jime imi`ig mebyiticib lribd lribd gi`issfaei aeblr.  pfaniwi sehit sehit tgi`isfaei ^fboibibyi ^fboibib yi pisefb tfrsfnut ebdeb afbecig. _ftf`ig me`icucib pfafrecsiib, oi`lb suiae mebyitic mebyiticib ib sfgi Aici cfaubdcebib ibicbyi icib afbdi`iae tgi`issfaei imi`ig sfnfsir: I. 6;% blr blrai` ai`,, 6; 6;% % pf pfani aniwi wi sseh ehit it ttgi` gi`iss issfae faei. i. N.

6; % afbmf afbmfreti reti tgi`i tgi`isfaei, sfaei, 6;% tpfa tpfaniwi niwi sehit sehit gi`iss gi`issfaei. faei.

O.

>6% tgi tgi`is `issfa sfaei, ei, > >6% 6% b blra lrai`, i`, 6 6;% ;% p pfan faniw iwi i seh sehit it

M. 9; 9;;% ;% a afb fbmf mfre reti ti tg tgi` i`is issf sfae aei. i.

 

Cfnfrgise`ib [fbofdigib ]gi`isfaei me nfrnidie Bfdiri

 

Cfnfrgise`ib [fbofdigib ]gi`isfaei me nfrnidie Bfdiri

Cfnfrgise`ib [fbofdigib ]gi`isfaei me Erib ‟   Me`icucib tibpi INL^_E

 

Cfseapu`ib •

]gi`isfaei afrupicib cf`ieibib mirig yibd sehitbyi meturubcib sfgebddi mipit meofdig mfbdib afbdgebmire pfrbecigib ibtir sfsiai pfaniwi dfb tgi`issfaei.

•

Vpiyi screbebd tgi`isfae afrupicib upiyi afbdgebmire cf`igerib niye tgi`isfaei.

•

Fmucise, slsei`esise, clbsu`tise sfnf`ua pfrbecigib itiu cfgiae`ib afrupicib upiyi yibd fhfcteh ubtuc afbebdcitcib cfsimirib af`icsibicib screbebd tgi`isfaei

 

]freai Ciseg

 

_li` #> Afbstruise pfbmfreti mic tfritur, neisibyi siapie 9; gire ip nu`ibbyi. Mire ibiabfses judi memipitcib nigwi enu pfbmfreti pfrbig afbmfreti ibfaei, tftipe mic pfrbig melni.

[fafrecsiib [fafrecs iib hsec ipi yibd aubdceb ubtuc Meidblses tgi`isfaei pimi pisefb ebe;9>

   

[FBUFNIN ]F^JIMEBUI CLA[@ECI_E<

FHFC [FBUICE]BUI: -

Ffots lh prlhlubm ibfaei Ebtriafmu``iry Ebtriaf mu``iry ibm -

fxtriafmu``iry fxpibselb fxtriafmu``iry ^ipem Erlb turblvfr ]essuf mfplselb lh fxofss fxofss erlb -

-

]M] ibm B]M]

]gi`issfaei ]ribshuse ]ribshuse ^uteb ]gi`issfaei ]ribshuse ]EMIC ^uteb

F H F C [ F B D L N I] I ]I B B U I : -

Ffots lh n`llm tribshuselb. _emf ffots lh erlb ogf`itlrs. Niotfrei` ebhfolbs

]M]

]gi`issfaei ]ribshuse ]ribshuse ^uteb

CLA[@ECI_E [IMI [I_EFB ]GI@I__FAEI

 

 

9>;

  l  b   r    E    `    i   E  B    )    )   s    e   l   b   b    ]   E   u   ^   h   s   ^   F   b   H   (    i     _  E  r   N  F   ]

9;; 7;    )   d    (     b   l   r    E

8;

   ]    I   Z     I  ^   M   C  I

=;

Mfitg Oirmeio hie`urf Gyplpiritgyrlemes a Gypltgyrlemesa Meinftfs Gypldlbimesa

>;

Oirmeio irrgytgaei Gfpiteo Henrlses --2 Oerrglses

; 9

?

6

4

5

99

 Idf (yfirs) (yfirs )

9 9? ?

9 96 6

9 94 4

9 95 5

]gi`issfaei Ofbtrf, Vbevfrsety lh ]lrebl

 

Clap`ecise tgi`issfaei ]gi`issfaei ]ribshuse ]ribshuse ^uteb

]gi`issfaei ]ribshuse ]EMIC ^uteb

Ausi``ia ft i`. Gifaitl`ldeoi >;9? 57: 7??-==.

 

[^EL^E]I_ ]I]I@IC_IBI Nfrmisircib V_EI

  b   i   s   u   e   d   m   d   f   b   A   i    D

  BFAE Drlwtg Hie`urf [llr Mfvf`lpafbt cf`fti` Mfhlraety

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BM E^LB LXF^@L M

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Ai`edbiboy Tlrcp`iof ibm Hebibo`i`

Airreidf ibm hiae`ey

]igfr ft i`. N`llm. >;9739?>(94):9479-9459

_urvevi` strfss

 

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