Pediatric

PEDIATRIC NURSING I. Growth & Development *Growth - Increase in physical size of a structure or whole. - Quantitative change. Two parameters of Growth 1.

Weight- Most sensitive measure of growth, especially low birth rate. 6 months-----BW doubles 12 months----BW triples 2-2 ½ yrs-----BW quadrupled

2. Height - Increase by 1”/mo during 1st 6 months, 7-12 months by 1 ½ inch. - Average increase in height - 1st year = 50% Stoppage of ht coincide with eruption of wisdom tooth. *Development - Increase skills or capability to function - Qualitative How to measure development: 1. Observe child doing specific task. 2. Role description of child’s progress 3. DDST- Denver development screening test except mental, its I.Q. Test MMDST (Phil) Metro Manila Developmental Screening Test. 4 Main Rated Categories of DDST 1. Language communication 2. Personal social-interaction 3. Fine motor adapting- prehensile ability to use hand movement 4. Gross motor skills- large body movement *Maturation- same with development “readiness” *Cognitive Development –ability to learn and understand from experience, to acquire and retain knowledge, to respond to a new situation and to solve problems. *Learning---change of behavior IQ Test- test to determine cognitive development Formula: Mental age x 100 = IQ Chronological age

* Average IQ – 90-100 * Gifted child- > 130 IQ

II. Basic Divisions of Life 1.

Prenatal stage from conception- birth

2.

Period of Infancy a. Neonate- 1st 28 days or 1st 4 weeks of life b. Formal infancy- 29 day – 1 year

3.

Early Childhood a. Toddler – 1-3 yrs b. Pre school 4-6 years

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Middle Childhood a. School age- 7 – 12 yrs

5.

Late Childhood a. Pre adolescent 11 – 13 yrs b. Adolescent 12 - 18 – 21

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III. Principles of G & D 1. G&D is a continuous process that begins from conception- ends in death--“ Womb to Tomb principle” 2. Not all parts of the body grow at the same time or at same rate.-------------“Asynchronous Growth principle” Patterns of G&D: a. b.

Renal, GIT, musculoskeletal, circulatory----grows rapidly during childhood Neuromuscular tissue (CNS, brain, S. cord)---grow rapidly 1-2 years of life  Brain achieved its adult proportion by 5 years.  1-2 y/o- very important yrs---if with severe malnutrition--mild mental retardation

c. Lymphatic system- lymph nodes, spleen, tonsils---grows rapidly- infancy and childhood -protection against infection  tonsil adult proportion by 5 years d. Reproductive system- grows rapidly at puberty Rates of G&D: a. Fetal and Infancy – period of most rapid G&D -----*prone to develop anemia b. Adolescent- period of rapid G&D Toddler- slow growth period c. Toddler and preschool- alternating rapid and slow d. School age- slower growth 3. Each child is unique A. Heredity:

2 Primary Factors Affecting G&D : R – race F- born less in length than M by 1 inch. I – intelligence F- born less in wt. than M by 1 lb. S – sex N - nationality

B. Environment: Q – quality of nutrition S – socio eco. status H – health O – ordinal position in family P – parent child relationship

Eldest- ability in comm. & social skills youngest- more toilet trained

4. G&D occurs in a regular direction reflecting a definitive & predictable patterns or trends. A. Directional Trends- occur in a regular direction reflecting the development of neuromuscular function. These apply to physical, mental, social and emotional development and includes. 1. Cephalo-caudal--- “head to toe”  Occurs along body’s long axis in w/c control over head, mouth & eye movements & precedes control over upper body torso and legs. 2. Proximo- distal---- “Centro distal”  From center of body to extremities. 3. Symmetrical----side of body develop on same direction at same time at same rate. 4. Mass Specific “Differentiation” - Learns simple operations before complex function, from broad general pattern of behavior to a refined pattern. B. Sequential- involves a predictable sequence of G&D to w/c the child normally passes. 1. Locomotion- creep, crawls, sit then stand. 2. Socio & Language skills- solitary games, parallel games C. Secular- worldwide trend of maturing earlier & growing larger as compared to succeeding generations. 5.Behavior--most compressive indicator of developmental status. 6. Universal language of child- play 7. Great deal of skill and behavior is learned by practice. Practice makes perfect. 9. Neonatal reflexes must be lost 1st before dev’t can proceed. -Plantar reflex shld. disappear before baby can walk

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*1st cry--oha 2nd sound-cooing 3rd sound-ahh(bowel) *1st play-solitary

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-Moro reflex shld. disappear before baby can roll *Persistent primitive infantile reflexes- case of cerebral palsy

IV. Theories of G&D Developmental Tasks- different from chronological age  skill or growth responsibility arising at a particular time in the individual’s life.  The successful achievement of w/c will provide a foundation for the accomplishments of future tasks. Theorists 1. SIGMUND FREUD: (1856-1939) Austrian neurologists----- Founder of Psychoanalysis - offered personality development, Psychosexual theory *Phases of Psychosexual Theory* a.) Oral Phase------------- 0-18 months - Mouth: site of gratification -Activity of infant- biting, sucking crying. -Why do babies suck?- enjoyment & release of tension. -Provide oral stimulation even if baby on NPO. -Pacifier. -Never discourage thumb sucking. b.) Anal Phase------------- 18 months-3 years -Anus: site of gratification -Activity- elimination, retention or defecation of feces must take place - Principle of holding on or letting go. -Mother wins or child wins -Child wins- stubborn, hardheaded anti social. (anak pupu na, child holds pupu, child wins) -Mother wins- obedient, kind, perfectionist, meticulous--------- OC-anal phase -Help child achieve bowel & bladder control even if child is hospitalized. c.) Phallic Phase----------- 3-6 years - Genitals: site of gratification - Activity- may show exhibitionism - Increase knowledge of a sexes - Accept child fondling his/her own genitalia as normal exploration - Answer Childs question directly. - Right age to introduce sexuality – preschool d.) Latent Phase---------- 7-12 years -Period of suppression- no obvious development. -Childs libido or energy is diverted to more concrete type of thinking -Helps child achieve (+) experience, ready to face conflict of adolescence e.) Genital Phase--------- 12-18 years -Genitals: site of gratification -Achieve sexual maturity -Learns to establish relationships with opposite sex. -Give an opportunity to relate to opposite sex. 2. ERIC ERICKSON- Psychoanalysis theory -stresses important of culture & society to the development of ones personality -environment , culture *Stages of Psychosocial Theory*

a.) Trust vs. Mistrust – 0-18 months. -foundations of all psychosocial task -to give & receive is the psychosocial theme -know to develop trust baby 1. Satisfy needs on time - breastfeed 2. Care must be consistent & adequate

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-both parents- 1st 1 year of life 3. Give an experience that will add to security- touch, eye to eye contact, soft music. b.) Autonomy vs. Shame & Doubt---- 18-3 years - Independence /self gov’t - Develop autonomy on toddler ---1. Give an opportunity of decision making, offer choices. 2. Encourage to make decision rather than judge. 3. Set limits c. Initiative vs. Guilt------------------------ 4-6 years -Learns how to do basic things -Let explore new places & events -activity recommended- modeling clay, finger painting--enhance imagination & creativity & facilitate fine motor dev’t d. Industry vs. Inferiority------------------- 7-12 yrs -Child learns how to do things well -Give short assignments & projects e. Identity vs. Role Confusion or Diffusion 12-18 yrs -Learns who he/she is, what kind of person he/ she will become by adjusting to new body image and seeking emancipation from parents -Freedom from parents. f. Intimacy vs. Isolation-----------------------18-25 yrs. Up to 30 y/o -looking for a lifetime partner and career focus g. Generatively vs. Stagnation------------ 30-45 y/o h. Ego Integrity vs. Despair---------------45-65 & above 3. JEAN PIAGET- Swiss psychologists , pioneer work on dev.t of intelligence in children -develop reasoning power *Stages Of Cognitive Development* A. Sensory Motor------ 0-2 y/o -“Practical Intelligence”- words & symbols not yet available baby communicates thru senses & reflexes. Schema (Subdivision) 1. Neonate Reflex 2. Primary Circular Reaction

Age 1 month 1-4 months

3. Secondary Circular Reaction

4-8 months

4. Coordination of Secondary Reaction

8-12 months

5. Tertiary Circular Reaction

12-18 months (1-1 1/2yrs.)

6. Invention of new means thu mental combination---“Symbolic Representation”

18-24 months

Behavior All reflexes -Activity related to body -Repetition of behavior (ex. thumb sucking) -Activity not related to body -Discover object & person’s permanence -Memory traces present -Anticipate familiar events. -Exhibit goal directed behavior of permanence & separateness (search of lost toy, knows mom, throw & retrieve) -Use trial & error to discover places & events -“ invention of new means” -capable of space & time perception (hits fork, spoon on table or drops fork) -Transitional phase to the pre operational thought process.

B. Preoperational Thought---- 2-7 y/o Schema 1. Preconceptual

Age 2-4 yrs

2. Initiative

4-7 yrs

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Behavior -Thinking basically complete literal & static -Egocentric- unable to view others viewpoint -Concept of dying is only now -Concept of distance is only as far as they can see. -Concept of Animism: inanimate object is alive (-) reversibility concept- in every action there’s an opposite reaction or cause & effect Beginning of Causation

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C. Concrete Operational Thought------ 7-12 years 1. Can find solution to everyday problems with systematic reasoning. 2. *Aware concept of reversibility- cause & effect 3. Concept of Conservation – constancy despite of transformation. 4. Activity recommended- collecting & classifying: stamps, stationeries, dolls, rubber band markers. D. Formal Operational Thought--------- 12 and up. 1. Cognition achieved its final form 2. Can deal with past present & future 3. Have abstract & mature thoughts & formal reasoning. 4. Can find solutions to hypothetical problems with scientific reasoning. 5. Activity: talk time:-- will sort out opinions & current events. 4. KOHLBERG (1984) - recognized the theory of moral dev’t as considered to closely approximate cognitive stages of dev’t *Stages of Moral Development* A. Infancy – “Amoral, Pre-religious or pre-moral stage Age 1. Pre-conventional 2-3 yrs 4-7

Stage Level 1 1

Description -*Punishment/ obedience oriented (heteronymous morality) child does right cause a parent tells him or her to & to avoid punishment -Individualism. Instrumental purpose & exchange. Carries out action to satisfy own needs rather than society. -Will do something for another if that person does something for the child.

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2. Conventional 7-10

Level 3

10-12

-Orientation to interpersonal relations of mutuality. Child follows rules cause of a need to be a “good” person in own eyes & eyes of others. -Maintenance of social order fixed rules & authority. Child finds ff. rules satisfying. Follows rules of authority figures.

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3. Post-conventional Above 12 yrs

Level III 5 6

-Social contract, utilitarian level making perspectives. Follows standards of society fro the good of the people. Universal ethical principle orientation. Follows internalized standards of conduct.

V. DEVELOPMENTAL MILESTONES -Major markers of growth and dev’t 1. Period of Infancy: *Universal language of child----- Play a. Play- Solitary plays (non-interactive) Priority : Safety (toys: age appropriate) Main goal: Facilitate motor & sensory dev’t Ex. mobile, teeter, music box, rattle b. Fear- Stranger anxiety begin 7-8 months: peak 8 months diminishes 9 months c. Milestones:

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Neonate:

>Complete head lag >Largely reflex visual fixation for human race > Hands fisted with thumbs in > Cries w/o tears d/t undeveloped lacrimal glands

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1 month:

> Dance reflex disappears looks at mobile

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> Alert to sound, regards face >Looks at mobile, follows to midline >Holds head up when in prone >Social smile, cries with tears, baby coos “doing sound” >Closure of Frontal Fontanel ( 2-3 months) >Head lag when pulled to sitting position. >No longer clenches fist tightly > Follows object past midline > Recognizes

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2 months:

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3 months:

>Holds head & chest up when prone > Holds hand, open at rest >Hand regards, follows object past midline > Grasp & tonic-neck reflexes are fading > Reaches for familiar people & object > Anticipates feeding

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4 months:

>Head control complete >Turns front to back, needs space to turn > Laugh aloud, bubbling sounds

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5 months:

> Turn both ways “roll over” >Teething rings, handles rattle well >Moro reflex disappears ( 4-5 months) > Enjoys looking around environment

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6 months:

>Reaches out in anticipatory of being picked up *>Sits with support >Uses palmar grasp, handles bottle well >Eruption of 1st temporary teeth: 6-8 months: 2 lower incisors >Say vowel sounds “ah”, “oh” > Sucking reflex disappears >Recognizes strangers (6-7 months) peak 8 months, diminishes 9 months

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7 months:

>Transfer object from hand to hand >Likes object that are good size for transferring

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8 months:

>Sits without support >Peak of stranger anxiety >Planters reflex disappears 8-9 months in prep. for walking

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9 months:

> Creeps or crawls, needs space for creeping >Neat finger grasp reflex, probes with forefinger (finger feeds) >Combine 2 syllables “mama” & “dada”

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10 months: >Pull self to stand >Understands “no” >Responds to own name >Activity: peak a boo, pat a cake, can clap

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11 months: >Cruises >Stands with assistance >Walking while holding to crib’s handle > One word other than mama & dada

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12 months: >Stands alone, take 1st step >Walk with assistance >Drink from cup, cooperate in dressing >Says 2 words mama & dada >Pots & pans, pull toys, nursery rhymes >Imitates action, comes when called >Uses mature pincer grasp, throws object

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> Follows one-step with gesture 2. Toddler: a. Play: Parallel play- 2 toddlers playing separately -Provide with similar toys Ex. squeaky frog to squeeze, waddling duck to pull, trucks to push-push pull toy, building blocks, pounding peg, toys to ride on b. Fear: Separation Anxiety: begin 9 months, peak 18 months 3 Phases Of Separation Anxiety (in order) P- protect D- despair D- denial -don’t prolong goodbye -say goodbye firmly to develop trust- say when you will be back c. Milestones 

15 months: >Plateau stage >Walks alone *Lateness in walking---mild mental retardation >Puts small pellets into small bowl >Holds spoon well >Seats self on chair, creeps up stairs >Scribbles voluntarily, say 4 - 6 words

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18 months: >Height of possessiveness >Favorite word- “mine” >Bowel control achieved (bowel 1st before bladder) >No longer rotates spoon >Can run & jump in place >Walks up & down stairs holding railing or persons hand >1-20 words >Names 1 body part >Puts both feet on 1 step before advancing.

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24 months: >Terrible two’s >Can open doors by turning door knobs > Turn pages one at a time, removes shoes & pants >Unscrew lids >Can walk upstairs alone –using both feet on same step at same time >50-200 words ( 2 words sentences), knows 5 body parts >Daytime bladder control achieved (daytime 1st , then night time bladder) > Bring to MD (2-3) or when temporary teeth complete

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30 months or 2 ½ year: >Makes simple lines or stroke for crosses with a pencil >Can jump down from chairs >Knows full name >Copy a circle >Holds up finger to show age >Temporary teeth complete (deciduous teeth -20)

*Posterior Molar- last temporary teeth to appear >Beginning of toothbrush – 2-2 ½ yrs >Tooth brushing with little assistance 3 yrs , brushing alone – 6 yrs > The right time to bring to dentist- when temp teeth complete 

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36 months or 3 yrs: >Trusting 3 >Unbutton buttons (unbutton before learn to button) >Draw a +, learns how to share >Knows full name & sex (gender identity) >Speaks fluently, 300-900 words

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>Nighttime bladder control achieved >Ride a tricycle d. Characteristic Traits of Toddler 1. Negativistic- “NO!” -way to search for independence >Limit questions >Modify questions to a statement 2. Rigid, ritualistic & stereotype >Ritualism- to gain mastery 3. Temper Tantrums (most common) >Head banging, screaming, stamping feet, holds breath >Ignore behavior *Protruding abdomen-d/t underdeveloped abdominal muscles *Physiologic anorexia- d/t preoccupation with environment- food fads, short period of time >Loves rough & tumbling play >Loves toilet training >Failure of toilet training- unreadiness *Clues For Toilet Readiness: 1.) can stand, squat walk alone 2.) can communicate toilet needs 3.) can maintain dryness for 2 hours 3. Pre-Schoolers: a. Play : Associative or Cooperative Play >bahay-bahayan – play house >Role playing b. Fear : Body Mutilation or Castration >Fear of dark places, witches >Fear of thunder & lightning >Fear of ghosts

Draws by age: 2 1/2 3 4 5

c. Milestones 

*4 years old:> Furious 4 , noisy, aggressive, stormy > Can button buttons > Copy a square > Jumps & skips *Laces shoes > Vocabulary 1,500 > Knows 4 basic colors > Say songs or poem from memory

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5 years old: > Frustrating 5 > Copy a triangle > Draw a 6 part man > Imaginary playmates > 2,100 words > Jumps over low objects

d. Character Traits of Pre-Schooler: 1. Curious, creative imaginative, imitative 2. Favorite words- “why & how” 3. Complexes- identification to parent of same sex & attachment to parent of opposite sex Ex. Oedipal complex- girl to dad/boy to mom Electra complex- identification to mother (daughter-mother), attachment to father >Cause of incest marital discord e. Behavior Problems 1. Telling tall tales d/t over imagination 2. Imaginary friend- to release tension & anxieties 3. Sibling rivalry- jealousy to newly delivered baby. 4. Regression- going back to early stage Sx: >thumb sucking (should be oral stage only) >baby talk, bed wetting, fetal position

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5. Masturbation- sign of boredom -divert attention, offer a toy 4. School Age: a. Play: Competitive play Ex. Tug of war, track and field, basket ball b. Fear. 1. School Phobia -orient to new environment 2. Displacement from school -teacher and peer of same sex 3. Loss of Privacy -wants bra 4. Fear of Death: thinks death is reversible as sleep

*7-9yrs death is personified -death as permanent loss of life

c. Significant Person: Teacher, peer of same sex d. Significant Development -boys prone to bone fracture - mature vision 20/20 e. Milestones

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6 years old: >Temporary teeth begin to fall >Perm teeth appear- 1st molar 1st temp teeth- 5 months 1st perm teeth- 6 yrs >Year of constant motion > Common: green-stick fracture >Recognize all shapes >1st grade teacher becomes authority figure >Nail biting >Begin interest in God.

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7 years old; Age of Assimilation >Copy a diamond >Enjoys teasing and playing alone >Quieting down period

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8 years old: Expansive age >Smoother movement >Loves to collect objects >Count backwards > Normal homosexual

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9 years old: >Coordination improves >Tells time correctly >Hero worship >Stealing & lying are common >Takes care of body needs completely >Teacher finds this group difficult to handle

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10 years old: >Age of Special Talent >Writes legibly >Ready for competitive games >More considerate & cooperative >Joins orgs. >Well mannered with adult >Critical of adults

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11-12 y/o:

>Pre-adolescents >Full of energy & constantly active >Secret language are common >Share with friends secrets

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>Sense of humor present >Social & cooperative f. Character Traits of School Age: 1. Industrious 2. Modest 3. Can’t bear to lose- will cheat 4. Love collections- stamps *SIGNS OF SEXUAL MATURITY* Girls

Boys

I-inc size breast & genitalia (thelarche- 1st sign sexual at.

A-appearance axillary & Pubic hair

W- widening of hips

D-deepening of voice

A- appearance axillary & pubic hair ( adrenarche)

D- development of muscles

M- menarche- last sign sexual mat. Girls

I—increase in testes and penis size ( 1st sign sexual mat) P- production of viable sperm ( last sign sexual maturity)

5. Adolescent : a. Fear : 1. Obesity 2. Acne 3. Homosexuality 4. Death 5. Replacement from friends b. Significant Person: Peer of Opposite Sex c. Significant Development 1. experiences conflict bet. his needs for sexual satisfaction & societies expectation *Core Concern: Change of body image & acceptance of opposite sex * Hallmark of Adolescence: Nocturnal Emission (wet dreams) 2. Distinctive odor d/t stimulation of apocrine glands 3. Sperm is viable by 17 y/o 4. Testes & scrotum increase until age 17 5. Breast & female genitalia increase until age 18 d. Personality Traits Adolescents: 1. Idealistic 2. Very conscious with body image 3. Rebellious 4. Reformers, adventuresome e. Problems: 1. 2. 3.

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Vehicular accident Smoking Alcoholism

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4. 5.

Drug addiction Pre-marital sex

II. IMMEDIATE CARE OF NEWBORN 1st days of life: 1. 2. 3. 4. 5. 6. 7. 8.

Initiation and maintenance of respiration Establishment of extra uterine circulation Control of body temp Establishment of waste elimination Intake of adequate nourishment Prevention of infection Establishment of an infant-parent relationship Dev’t care that balances rest & stimulation or mental dev’t

1.) Initiation and Maintenance of Respiration 2nd stage of labor- initial airway -initiation of a /w is a crucial adjustment -most neonatal deaths w/n 24 h caused by inability to initiate a/w -lung function begins after birth only How to initiate a/w : a. Remove secretions bulb syringe b. Catheter Suctioning 1.) Place head to side to facilitate drainage of secretions 2.) Suction mouth 1st before nose -neonates are nasal breathers 3.) Period of time 5-10 sec suctioning, gentle and quick Prolonged & deep suctioning can lead to : Hypoxia Laryngospasm, Bradycardia d/t stimulation of vagal nerve--near esophagus & anus 4.) Evaluate for patency -cover nostril & baby struggles there’s a need for additional suctioning c. If not effective, requires effective laryngoscopy to open a/w. After deep suctioning an endotracheal tube can be inserted and oxygen can be administered by (+) pressure bag and mask with 100% oxygen at 40-60b/m. Nsg alert In O2 Administration: 1. No smoking to prevent combustion 2. Always humidify to prevent drying of mucosa 3. Over dosage of oxygen can lead to scarring of retina leading to blindness (Retro Lentalfibrolasia or Retinopathy of Prematurity) ROP---prone to:SGA,LBW,Preterm 4. When meconium stained (greenish) never administer oxygen with pressure (O2 pressure will push mecomium inside)------Atelectasis 2.) Establishing Extra-Uterine Circulation *Circulation is initiated by lung expansion or pulmo ventilation and completed by cutting of cord. FETO PLACENTAL CIRCULATION * Placenta(simple diffusion) –oxygenated blood is carried by the umbilical vein- passes liver-ductus venousus- IVCRT atrium 70% blood is shunted to foramen ovale- LT atrium mitral valve – LT ventricle- aorta-lower extremities.

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-Remaining 30%- tricuspid valve- RT ventricle- pulmonary arteries- lungs (for nutrition)--vasoconstriction of lungs pushes blood to ductus arteriousus to aorta to supply upper extremities. *3 SHUNTS* SHUNTS-shortcuts 1. Ductus Venosus- -shunts from liver to IVF (umbilical vein to inferior vena cava) 2. Foramen Ovale- shunts bet 2 atrias 3. Ductus Arteriosus- from pulmonary artery to aorta Decrease PO2, increase PCO2 acidosis

Will cause 1st breath /cry of baby

Decrease Pulmo Artery Pressure

Increase PO2

1. Closure of Ductus Arteriosus

Decrease blood flow

2. Closure of Ductus Venosus & AVA

Increase pressure to Left side of heart

3. Closure of Foramen Ovale

What will sustain 1st breath- decreased artery pressure What will initiate lung circulation-lung expansion What will complete circulation- cutting of cord 4.) 2 Ways to facilitate closure of Foramen Ovale a.) Tangential Footstep- slap foot of baby----slap---cry---lung expansion -never stimulate baby to cry if secretions not fully drained to prevent aspiration -check characteristic of cry *Normal cry- strong, vigorous and lusty cry *Normal cry of baby boy: lower cri-du-chat syndrome-chromosomal obliteration cat like cry (meow) b.) Proper position : Right side lying pos. -will increase pressure on left and foramen ovale will close *Foramen Ovale and Ductus arteriosus will begin to close within 24h *Universal Cry of a Baby: “O-ha” Obliteration-complete closure Structure Appropriate Time of Structure Remaining Obliteration Foramen Ovale Begins 24 hrs, 1yr Fossa Ovalis Ductus Begins 24 hrs., 1 month Ligamentum Arteriosum Arteriosus Ductus Venosus 2 months Ligamentum venosum 1.) Lateral umbilical Ligament Umbilical artery 2-3 months 2.) Interior iliac artery Umbilical vein 2-3 months Ligamentum Teres ( round ligament of liver)

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Failure to Close Atrial Septal Defect Patent Ductus Arteriosus

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*Position of infant immediately after birth: NSD-Trendelenberg/ T position for drainage contraindication of Trendelenberg position - increase ICP CS- Supine or crib level position

Signs of Increased ICP 1. Abnormally large head 2. Bulging and tense fontanel Hypertension 3. BP and widening pulse pressure Bradycardia Cushing’s Triad of ICP 4. RR & PR Tachypnea 5. Projective Vomiting- sure sign of cerebral irritation 6. High deviation – Diplopia – sign of ICP older child 4-6 months- normal eye deviation if >6 months- lazy eyes 7.) High pitch shrill cry- late sign of ICP 3. Control of Body Temperature : Temp Regulation -

*Goal in temp regulation is to maintain it not less than 97.7% F (36.5 C) Maintenance of temp is crucial on preterm and SGA (small for gestational age) - babies prone to hypothermia or cold stress

A. Factors Leading to Dev’t of HYPOTHERMIA 1.

2. 3. 4.

Preterms are born PoiKilothermic- cold blooded  Babies easily adapt to temp of environment d/t immaturity of thermo regulating system of body. >Hypothalamus Inadequate SQ tissue fats Baby is not capable of shivering *Earliest sign of hypothermia- increase in RR Babies are born wet PROCESS OF HEAT LOSS 1. Evaporation------body to air (TSB) 2. Conduction------body to cold solid object (cold compress) 3. Convection------body to cooler surrounding air (aircon) 4. Radiation-------- body to cold object not in contact with body

Effects of Hypothermia ( Cold stress) 1.) Hypoglycemia- 45-55 mg/dl normal ( 50- borderline) d/t utilization of glucose 2.) Metabolic acidosis- catabolism of brown fats (best insulator of newborns body) will form ketones ( found in chest/back) 3.) High risk for kernicterus- bilirubin in brain leading to cerebral palsy 4.) Additional fatigue to allergy stressful heart To Prevent Hypothermia: 1. Dry and wrap baby 2. Mechanical pressure – radiant warmer (incubator) *Pre-heat first isolette (or square acrylic sided incubator) 3. Prevent an necessary exposure – cover baby 4. Cover baby with tin foil or plastic 5. Embrace the baby- kangaroo care (skin to skin contact) 4. Establish Adequate Nutritional Intake Physiology Breast Milk Production: As you deliver baby, E &

Physiology of Breast Milk Release: Sucking of the Breast

P

APG releases: Prolactin

Posterior P. G. releases Oxytocin

w/c acts on Acinar Cells/Alveoli To Produced foremilk

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Contraction of smooth muscles of the Lactiferous tubules

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Stored in lactiferous Tubules (or Collecting Tubules)

Milk Ejection Reflex

Let-Down Reflex

*CS- breastfeeding after 4 hours *NSD- breastfeeding asap *Advantages of Breastfeeding *Store milk- plastic storage container 1. Economical >good for 6 mon. from freezer/ at rm. temp. don’t heat 2. Always available 3. Promotes Bonding 4. Breastfed babies have higher IQ than bottle fed babies. 5. It facilitates rapid involution 6. Decrease incidence of breast cancer. 7. Contents of BREAST MILK: a. Antibodies- IgA b. Lactobacillius bifidus- interferes w/ attack of pathogenic bacteria in GIT c. Has macrophages d. Lactoferrin e. Lyzozymes f. Interferons Disadvantages: 1. Possibility of transfer HEP B, HIV ( 30%-39%), cytomegalovirus virus. 2. No iron-----prone to IDA 3. Father can’t feed & bond as well 3 Stages of Breastmilk: 1. Colostrum- 2-4 days post-delivery content: fats, IgA, CHO, CHON, minerals, fat soluble minerals 2. Transitional milk- 4 – 14 days content: lactose, water soluble vit., minerals 3. Mature milk- 14 & up (3 L) content: fats (linoleic acid) – resp for devt of brain & integrity of skin CHO- lactose – easily digested, baby not constipated. - responsible of sour milk smelling odor of stool & astringent property of milk *Lactose Intolerance- deficiency of enzyme LACTASE that digests LACTOSE —manifestation = Excessive Crying ------substitute-----soy milk *Decrease CHON- lactalbumin Contents of Cows milk: fats CHON – casein- has curd that’s hard to digest Minerals–traumatic effect on kidneys of babies. Can trigger stone formation. Phosphorus CHO 5. Prevention of Infection: Health Teachings: 1. Proper hygiene- proper hand washing Care of breast - cotton balls with lukewarm water (inner to outer) Caked colostrums- dry milk on breast 2. Best position in breastfeeding – upright sitting -avoid tension!—if w/ tension breast will not properly empty 3. Stimulate & evaluate feeding reflexes a.) Rooting reflex- by touching the side of lips/cheeks then baby will turn to stimulus. Disappear by 6 weeks- by 6 weeks baby can focus. Reflex will be gone - Purpose rooting- to look for food. b.) Sucking – when you touch middle of lips then baby will suck - Disappears by 6 months - When not stimulated sucking will stop. c.) Swallowing- when food touches posterior of tongue then it will be automatically swallowed d.) Extrusion/ Protrusion reflex -when food touches anterior portion of tongue then food will be extruded. Purpose: to prevent from poisoning

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Disappear by 4 months & baby can already spit out by 4 months. Criteria Effective Sucking: a.) Baby’s mouth is hiked up to areola b.) Mom experiences after pain. c.) Other nipple is also flowing with milk. To prevent from crack nipples & initiate proper production of oxytocin. - begin 2-3 min at per breast ( 5 – 7 min other authors) to initiate production of oxytocin - increase 1 min/ day – until reaching 10 mins per breast or 20 mins/ feeding. For proper emptying & continuous milk production / feeding -feed baby on last breast that you feed her with, alternately ( if not emptied - mastitis) Problems Experienced in Breastfeeding : 1st day post-partum: Breast soft & tender 3RD day changes in breast post partum: a.)Engorged- feeling of fullness & tension in breast. - sometimes accompanied by fever known as MILK FEVER-continue BF Mgt: Warm compress- for breastfeeding mom Cold compress – for bottle feeding & wear supportive bra. *When is involution of breast? - 4 weeks b.) Sore nipple – cracked with painful nipple Mgt: Exposure to air – remove bra & wear dress, if not, expose to 20 Watt bulb (12-18 inches away) avoid wearing plastic liner bra - will create moisture, cotton only----continue BF c.) Mastitis- inflammation of breast : staphylococcus aureus (common) Factors: 1. Improper breast emptying 2. Unhealthy sexual practices -contraindicated for breast feeding - manually express inflamed breast----- feed on unaffected breast - give antibiotics – can still feed on unaffected breast Contra Indications in Breast Feeding: a. Maternal Conditions: >HIV >CMV >Hep. B > Coumadin

b. Newborn Condition: Inborn errors of metabolism Erythroblastosis Fetalis – Rh incompatibility Hydrops Fetalis, Tay Sachs disease Phenylketonuria, Galactosemia

6. Establish Waste Elimination A. Different Stools 1. Meconium - physiologic stool - black green, sticky, tar like, odorless (Sterile intestine)(no bacteria) will pass w/in 24 – 36 hrs *Failure to pass mecomium after 24h- GIT obstruction ex. Hirschsprungs disease Imperforate anus Mecomium ileus – due to Cystic Fibrosis 2. Transitional Stool - (4-14 days) - green loose & shiny, like diarrhea to the untrained eye (primipara mother) *3. Breastfed Stool - golden yellow, soft, mushy with sour milk smell, frequently passed - recur every feeding (orange-yellow) 4. Bottlefed Stool - pale yellow, formed hard with typical offensive odor, seldom passed, 2–3 x/day 5. Supplementary - with food added -brown & odorous Indication of Stool Changes:

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Jaundice baby – Under phototherapy – Mucus mixed with stool *Clay colored stool – Chalk clay stool – Black stool – Blood flecked stool -

light stool bright green milk allergy obstruction to bile duct after barium enema GIT bleeding (melena) anal fissure.

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*Currant jelly stool – *Ribbon like stool – Cult blood – *Steatorrhea stool –

intussuseption hirschsprung disease stool exam fatty, bulky foul smelling odor stool  malabasorption syndrome (Celiac disease or Cystic fibrosis)

III. ASSESSMENT FOR WELL-BEING A. APGAR SCORE – Dr. Virginia Apgar Special Considerations:

1st 1 min – determine general condition of baby Next 5 min- determine baby’s capabilities to adjust extra uterinely (most important) Next 15 min – dependent on the 5 min

A- appearance- color – slightly cyanotic after 1st cry baby becomes pink. P- pulse rate – apical pulse – left lower nipple G- grimace – reflex irritability- (1) tangential foot slap, (2) catheter insertion A – activity – degree of flexion or muscle tone R – respiration Baby cry – within 30 secs Failure to cry after 30 secs – asphyxia neonatorum Resp. depression – d/t mom given Demerol. Administer Naloxone

HR (most important) Respiratory Effort Muscle Tone

APGAR Scoring Chart: 0 1 Absent 100 Good strong cry Well flexed Cough, sneeze Cry Pinkish

APGAR Result: 0 – 3 = severely depressed, need CPR, admission NICU 4 – 6 = moderately depressed, needs add’l suctioning & O2 administration 7 - 10 =good/ healthy CPR – cardio pulmonary resuscitation or CPR New: Cardio pulmonary cerebral resuscitation (CPCR) 5 min no O2 – irreversible brain damage a/w 1. shake, no resp, call for help 2. flat on head, use cardiac board 3. head tilt chin lift maneuver except spinal cord injury over extension may occlude airway Breathing ( ventilating the lungs) 1. check for breathlessness if breathless, give 2 breaths- ambu bag > 1 yr old- mouth to mouth, pinch nose to create a seal < 1 yr – mouth to nose Force – different between baby & child infant – puff Circulation :

Check for pulselessness : carotid- adult Brachial – infants

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CPR – breathless/pulseless Compression –for infant: 1 finger breath below nipple line or 2 finger breaths or thumb CPR :

Infant 1:5 Adults 2:15

B. Respiration Evaluation 1. Assessment tool that determines respiration of baby : Silvermann Anderson Scale Criteria Chest movement Intercostal retraction Xiphoid retraction Nares dilatation Expiratory grunt

0 synchronized No retraction None None None

1 Lag on respiration Just visible Just visible Minimal Heard on stet only

2 See - saw Marked Marked Marked Heard on naked ear Lowest score –

best Interpretation result: 0 -3 – normal, no RDS 4 – 6 – moderate RDS 7 – 10 – severe RDS C. Assessment of Gestational Age 1. Clinical Criteria: Ballards & Dobowitz Findings Less 36 weeks (Preterm) 37 - 38 Sole creases Anterior transverse crease Occasional creases 2/3 only in Breast nodules 2mm 4mm or 3.5 mm Scalp hair Fine & fuzzy Fine & fuzzy Ear lobe Pliable Some cartilage Testes and Scrotum testes in lower canal Some intermediate Scrotum – small few rugae

39 and up Covered with creases > 5 or 7mm Coarse & silky Thick cartilage Testes pendulus Scrotum fully covered w/ rugae

*2. Signs of Preterm Babies > Born after 20 weeks & before 37 weeks >Frog leg or lax position >Hypotonic muscle tone- prone resp problem >Scarf sign – elbow passes midline pos. >Square window wrist – 90 degree angle of wrist >Heel to ear sign Complications: RDS, Hypothermia, ROP >Abundant lanugo *Type of Feeding Pre-Term: Gavage Feeding –to prevent aspiration –d/t absence of gag & swallowing reflex *3. Signs of Post term babies: > 42 weeks >Classic sign – old man’s face >Desquamation – peeling of skin *Long brittle finger nails >Wide & alert eyes

IV. Neonates in Nursery 1. Special & Immediate Interventions: a. Nsg responsibility upon receiving baby- proper identification - Foot printing, affixing mother thumb print b. Take anthropometric measurement normal length- 19.5 – 21 inch or 47.5 – 53.75cm, average 50 cm head circumference 33- 35 cm or 13 – 14 “ Hydrocephalus - >14” Chest 31 – 33 cm or 12 – 13” (Average 32 cm)

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Abdomen 31 – 33 cm or 12 – 13” c. Bathing >Oil bath – initial : To cleanse baby & spread vernix caseosa Fx of vernix caseosa : 1. Insulator 2. Bacterio- static * Babies of HIV + mom – immediately give full bath to lessen transmission of HIV (13 – 39% possibly of transmission of HIV *Full bath – safely given when cord fall *Dressing the Umbilical Cord: strict asepsis to prevent tetanus d. Dressing the Umbilical Cord 1. * 3 Cleans in community 1. Clean hand 2. Clean cord 3. Clean surface Betadine or Povidone Iodine – to clean cord 2. Check AVA, then draw 3 vessel cord--- if 2 vessel cord—suspect absence of kidneys - leave about 1 inch” of cord - if BT or IV infusion – leave 8” of cord *Best site of blood nerve access: umbilical cord 3. Check cord every 15 min for 1st 6 hrs – bleeding .> 30 cc of blood----hemorrhage *Excessive bleeding of cord – Omphalagia – suspect hemophilia or blood dyscrasias *Cord turns black on 3rd day & fall 7 – 10 days *Failure to fall after 2 weeks- Umbilical granulation (w/o foul smelling odor, pinkish) Mgt: silver nitrate or cautery - clean with normal saline solution not alcohol - don’t use bigkis – air - persistent moisture-urine, suspect patent uracus – fistula bet bladder & normal umbilicus Dx:

Nitrazine paper test – if yellow – urine ---if blue – amniotic fluid - if reddish -- Omphalitis Mgt: Surgery e. Credes Prophylaxis – Dr. Crede Purpose: prevent opthalmia neonatorum or gonorrheal conjunctivitis * how transmitted – mom with gonorrhea or chlamydia Drug: erythromycin ophthalmic ointment- inner to outer Silver nitrate (used before) – 2 drops lower conjunctiva (not used now) -causes staining of skin, chemical conjunctivitis - does not give protection against STDs f. Administer Vit-K – to prevent hemorrhage R/T physiologic hypoprothrombinemia - Aquamephyton, phytomenadione or konakion - .5 – 1.5 mg IM, vastus lateral or lateral ant thigh - 5 mg preterm baby *Vit K – synthesized by normal flora of intestine Vit K – meds is synthetic d/t intestine is sterile g. Weight-taking > Normal wt 3.000 – 3400 gms/ 3 – 3.4 kg / 6.5 > Arbitrary lower limit 2500 gm > Low birth wt baby delivered < 2500g

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7.5 lbs

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> Small for gestational age (SGA) < 10th % rank or born small > Large for gestational age > 90th % rank or macrosomia >4000 g > Appropriate for GA – within 2 standard deviation of mean (AGA) > Physiologic wt loss – 5 – 10% wt loss few days after birth Small GA < (less) 10 Large GA > (more) 90 V. PHYSICAL EXAM & DEVIATIONS FROM NORMAL A. Important Considerations: 1. if client is new born, cover areas not being examined to prevent hypothermia 2. if client is infant – the 1st yr of life - get VS – take RR 1st - begin from least intrusive to the most intrusive area 3. if client is a toddler and preschool, let them handle an instrument like: - play syringe or stet, security blanket – favorite article. Let baby hold it, allow bedtime rituals 4. Explain procedure & respect their modesty - school age & adolescent - by wearing your complete uniform *Security Blanket--- a transitional object as representation of the parents B. Components: 1. V/S: Temp: rectal- newborn – to rule out imperforate anus/assess patency of anus - take it once only, 1 inch insertion Imperforate anus 1. Atretic – no anal opening more dangerous 2. Agenetic – no anal opening 3. Stenos – has opening but narrow opening 4. Membranous – has opening Earliest sign: 1. No mecomium 2. Abdominal destention 3. Foul odor breath 4. Vomitous of fecal matter 5. Can aspirate – resp problem may arise d/t aspiration of intestinal contents----atelectasis Mgt: Surgery with temporary colostomy Cardiac rate: 120 – 160 bpm newborn Apical pulse – left lower nipple Radial pulse – normally absent. If present PDA (+) radial pulse Femoral pulse – normal present. If absent- COA - coartation of aorta

Congenital Heart Diseases: *Common in girls – PDA, ASD , Atrial Septal (Acyanotic HD) *Common in boys – TOGA ( Transposition of great arteries) TA – Tronchus arteriosus TOF – Tetralogy of Fallot *Causes: 1. Familial 2. Exposure to rubella – 1st month of pregnancy 3. Failure of heart structure to progress

Cyanotic HD

2 Major Types: “AL CR” 1. Acyanotic L to R : Left to Right shunting 2. Cyanotic R to L : Right to Left shunting I. ACYANOTIC HEART DEFECTS L to R ---------( 8 Types) *With increased pulmonary blood flow 1. Ventricular Septal Defect (VSD ) - opening between 2 ventricles S&Sx:

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a. Systolic murmurs at lower border of sternum and no other significant sign b. Cardiac catheterization reveals increased o2 saturation @ R side of heart c. ECG reveals hypertrophy of R side of heart Nsg Care: Cardiac catheterization: site – Right femoral vein 1. NPO 6 hrs before procedure 2. Protect site of catheterization. Avoid flexion of joints proximal to site. 3. Assess for complication – infection, thrombus formation – check pedal pulses Mgt. 1.) *Long term antibiotic – to prevent subacute bacterial endocarditis 2.) Open heart surgery 2.) Atrial Septal Defect (ASD) – Failure of foramen ovale to close S & Sx: 1. Systolic murmur @ upper border of sternum 2. Result of cardiac catheterization & ECG same with VSD-- O2 sat & hypertrophy Mgt: Open heart surgery 3.) Endocardial Cushion Defects (ECD) - atrium ventricular - affects both tricuspid & mitral valve Dx Mgt:

: Confirmed by cardiac catheterization : Open heart surgery Antibiotics to prevent subacute bacterial endocarditis

4.) Patent Ductus Arteriosus - Failure of ductus arteriosus to close - should close within 24 h -complete close – 1 month S & Sx : 1. Continuous machinery like murmurs > outstanding sign of acyanotic HD 2. Prominent radial pulse 3. ECG- hypertrophy Left ventricle Drug: 1. Endomethacine – prostaglandin inhibitor - facilitate closing of PDA 2. Ligation of PDA by 3-4 y/o via thoracotomy procedure- nakadapa child *With decrease Pulmonary Blood Flow 5.) Pulmonary Stenosis- narrowing of valve of pulmonary artery S &Sx: 1. Typical systolic ejection murmur---d/t congestion at the right side of heart 2. S2 sound widely split 3. ECG- R. ventricular hypertrophy *Normal: Pulmonary Artery = size with aorta* 6.) Aortic Stenosis – narrowing of valve of aorta S & Sx: 1. If inactive, sx same with angina-like symptoms 2. Typical murmur 3. Rough systolic sound and thrill 4. ECG- Left ventricular hypertrophy Cardiac catheterizationMgt. For Pulmonary Stenosis & Aortic Stenosis---ECMO>Extra Corporeal Membrane Oxygenation -a lung & heart machine - return to activity: 3 wks. 1.) Balloon Stenotomy 2.) Surgery 7. Duplication of Aortic Arch- doubling of arch of aorta causing compression to trachea & esophagus S & Sx : 1. Dysphagia 2. Dyspnea 3. left ventricular hypertrophy

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Mgt: Close heart surgery *8. Coartation of Aorta – narrowing of arch of aorta *Outstanding Sx : Absent Femoral Pulse BP increased on upper extremities & decreased on lower extremities ECG – hypertrophy Left ventricle ------EPISTAXIS Mgt: close heart surgery Monitor BP on 4 extremities II. CYANOTIC HEART DEFECTS R to L (6) *With increase Pulmonary Blood Flow 1. Transportation of Great Arteries (TOGA) - aorta arising from Rt ventricle, pulmo artery arising form Lt ventricle - direct from RV to aorta w/o oxygenation Outstanding Sx: 1. Cyanosis after 1st cry (due no oxygenation) 2. *Polycythemia – increased RBC =compensatory d/t O2 supply=viscous blood *Complications: Thrombus = Embolus = Stroke 3. ECG – cardiomegaly 4. Cardiac cath – decreased O2 saturation 5. Palliative repair – rash kind procedure 6. Complete repair – mustard repair 2.) Total Anomalous Pulmonary Venous Return – pulmo vein instead of entering Lt atrium, enters Rt atrium or SVC Increased pressure on Rt so blood goes to Left Outstanding Sx: Open Foramen Ovale -------so blood L to R >Mild to moderate cyanosis >Polycythemia = thrombus = embolus = stroke >Asplenia- absent spleen Mgt: Restructuring of heart 3.) Truncus Arteriousus - aorta & pulmo artery is arising from 1 single vessel or common trunk with VSD S & Sx 1. Cyanosis 2. Polycythemia – thrombus = embolus = stroke Mgt: Heart transplant 4.) Hypoplastic Left Heart Syndrome – a non- functioning Left ventricle S & Sx: 1. Cyanosis 2. Polycythemia – thrombosis, embolus, stroke Mgt: Heart Transplant *With decrease Pulmonary Blood Flow 5.) Tricuspid Atresia – Failure of tricuspid valve to open S&SX: 1. Open Foramen Ovale-----pressure increase in right so open FO (R to L shunting – goes to Lt atrium) 2. Cyanosis, Polycythemia Mgt: Fontan procedure – to open tricuspid valve 6.) Tetralogy Of Fallot (TOF) P – pulmonary stenosis V – ventricular SD O – overriding or dextroposition of aorta R – Rt ventricular hypertrophy S &Sx: 1. 2. 3. 4. 5. 6. 7. 8.

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Rt ventricular hypertrophy High degree of cyanosis Polycythemia Severe dyspnea – squatting position – relief , inhibit venous return, facilitate lung expansion. Growth retardation – due no O2------ Mental retardation –d/t O2 in brain Tet spell or blue spells- short episodes of hypoxia—blue baby esp. when crying Syncope Clubbing of fingernails – due to chronic tissue hypoxia

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9.

Boot shaped heart – revealed by x-ray

Mgt: 1. 2. 3. 4.

O2 administration after 1 month old—to wait for the complete closure of the ductus arteriosus No valsalva maneuver , fiber diet laxative Morphine – hypoxia , Propanolol – decrease heart spasms Palliative repair – BLT >Blalock taussig procedure Brock procedure – complete procedure

ACQUIRED HEART DISEASES 1. Rheumatic Heart Disease (RHD) - inflammation disease ff an infection acquired by group A Beta hemolytic streptococcus (GABHS) a. Affected body – cardiac muscles and valves , musculoskeletal , CNS, Integumentary b. Suspect : Sorethroat before RHD -----candidate babies---eating lots of sweets c. Aschoff – rounded nodules with nucleated cells & fibroblasts – stays that occludes mitral valve. d. To Diagnose RHD uses the Jones Criteria

*Jones Criteria* Major 1. Polyarthritis – multi joint pain 2. Chorea – Sydenhamms Chores or St. Vitous Dance -purposeless involuntary hand and shoulder with grimace 3. Carditis – characterized by tachycardia 4. Erythema marginatum - macular rashes 5. SQ nodules

Minor 1. Arthralgia – joint pain 2. Low grade fever 3. All Dx Test & Lab results antibody C reactive protein Erythrocyte sedimentation rate Anti streptolysin O titer (ASO)

*Criteria: Presence of 2 major, or 1 major & 2 minor + history of sore throat will confirm the dx. Mngt: Supportive only Nsg Care: 1. CBR , avoid contact sports 2. Throat swab – culture & sensitivity for antibiotic therapy 3. *Antibiotic mgt – to prevent recurrence 4. Aspirin ( ASA therapy)– anti-inflammatory. Low grade fever – don’t give aspirin. S/E of aspirin: if given to children continuously w/ bacterial infection: *Reyes syndrome – encephalopathy- fatty infiltration of organs such as liver & brain 2. Respiration Newborn resp – 30-60 cpm, irregular abd or diaphramatic with short period of apnea w/o cyanosis. If < 15 secs – normal apnea –newborn , if >15 secs. ---dead already Resp Check: Newborn – 40 – 90 bpm 1 yr - 20 – 40 2-3yr 20 – 30 5 yrs 20 – 25 10 yrs 17 – 22 15 & above 12- 20 BREATH SOUNDS HEARD DURING ASCULTATION: Sound 1. VESICULAR : 2. BRONCHOVESICULAR:

Characteristics Soft, low pitched, heard over periphery of lungs, inspiration longer then expiration -Normal Soft, medium pitched, heard over major bronchi, inspiration equals exp. Normal

3. BRONCHIAL SOUNDS: Loud high pitched, heard over trachea, expiration longer than inspiration. Normal 4. RHONCHI : 5. RALES:

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Snoring sound made by air moving through mucus in bronchi. Normal or crackles – like cellophane – made by air moving through fluid in alveoli. Abnormal- pneumonia, pulmonary edema

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6. WHEEZING: 7. STRIDOR: 8. RESONANCE: 9. HYPERRESONANCE:

Whistling on expiration made by air being pushed through narrowed bronchi Abnormal – asthma, foreign body obstruction Crowing or rooster life sound – air being pulled through a constricted larynx. Abnormal – resp obstruction, inspiratory stridor Loud, low tone, percussion sound over normal lung tissue Louder, lower sound than resonance, a percussion sound over hyperinflated lung tissue

1. Asthma Pathognomonic Sign: Expiratory wheezing Pet – fish. Sport – swimming Drugs – Aminophylline – monitor BP, may lead to hypotension Allergens: dust Food allergens: seafood, chocolate, Climate Changes 2. Respiratory Distress Syndrome (RDS) or Hyaline Membrane Cause- lack of surfactant – for lung expansion ----------------end stage: Atelectasis Hypotonia, Post surgery, Common to preterm Fibrine Hyaline : Sx----definite with in 1st 4 hrs. of life ---d/t lack of surfactant Tachypnea with retraction -------earliest sign *Inspiratory Grunting – Pathognomonic Sx > 7 – 10 severe RDS (Silverman Anderson Index), respiratory acidosis end stage: Cyanosis d/t atelectasis *Chromolin Sodium---prevents asthmatic attack before attack administer > if with asthma attack ----bronchodilator---Aminophylline—monitor BP Mgt: 1. Surfactant replacement and rescue 2. Pos- head elevated 3. Proper suctioning 4. O2 with increase humidity- to prevent drying of mucosa 5. Monitor V/S skin color , ABG------R.A. 6. 7.

*CPAP- continuous (+) a/w pressure PEEP - + end expiratory pressure Purpose of #6-7- to maintain alveoli partially open & alveoli collapse

3. LaryngoTracheo Bronchitis (LTB) Pathognomonic Sign: Inspiratory Stridor LTB – most common Creup -viral infection of larynx, trachea & bronchi Outstanding Sx : Croupy cough or barking - Labored respiration - Respiratory acidosis - End stage – death Lab: 1. ABG 2. Neck and throat culture 3. Dx- neck x-ray to rule out epiglotitis 4. CBC- to determine leukocytosis Nsg Mgt: 1. Bronchodilators 2. Humidified oxygen 3. Prepare tracheostomy set 4. Corticosteroids 4. Broncholitis Inflammation of bronchioles characterized by production of thick, tenacious mucus *Causative agent – RSV - Resp sincytial virus Sx: Flu-like sx Increased RR---Monitor: Tachypnea of >90 bpm =RDS Drug: Antiviral – Ribavirin End stage – epiglotitis 5. Epiglotitis Inflammation of epiglottis

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*Emergency: Condition of URTI Sx: *Sudden onset *Tripod Position – leaning forward with tongue protrusion *Never use tongue depressor >Prepare tracheotomy set *< 5 y/o – unable to cough out, put on mist tent (humidifier o2) or croupe tie Nsg Care: Check edges tucked on mist tent Provide washable plastic material No toys with friction due O2 on No hairy toys – due moist environment medium for bacterial growth No smoking 2.Blood Pressure BP – 80/46 mmHg newborn BP after 10 days- 100/50 BP taking begins by 3 y/o COA – take BP on 4 extremities 3. Skin / Integumentary *Acrocyanosis Birthmarks: 1. 2. 3. 4. 5. 6. 7. 8. 9.

Mongolian Spots: stale gray or bluish discoloration patches commonly seen across the sacrum or buttocks d/t accumulation of melanocytes. Disappear by 1 yr old or 5 y/o pre-schooler Milia – plugged or unopened sebaceous gland, white pin point patches on nose, chin or cheek. Lanugo – fine, downy hair – common preterm Desquamation – peeling of newborn, extreme dryness that begin sole and palm. Stork bites (Telangiectasis nevi) – pink patches nape of neck  hair will grow as child grows old Erythema Toxicum – (flea bite rash)- 1st self limiting rash appear sporadically & unpredictably as to time & place. Harlequin Sign – dependent part is pink, independent part is blue (side lying – bottom part is dependent pink) Cutis Marmorato – transitory mottling of neonates skin when exposed to cold. Hemangiomas – vascular tumors of the skin

3 Types of Hemangiomas a.) Nevus Flammeus – port wine stain – macular purple or dark red lesions seen on face or thigh. NEVER disappear. Can be removed surgically b.) Strawberry hemangiomas – nevus vasculosus – dilated capillaries in the entire dermal or subdermal area. Enlarges, disappears at 10 y/o. c.) Cavernous hemangiomas – comm. network of venules in SQ tissue that never disappear with age. MOST DANGERIOUS – intestinal hemorrhage 10. Vernix Caseosa – white cheese like for lubrication, insulator Skin Color & its significance: Blue – cyanosis or hypoxia Ringworm Infestation: White – edema Tinea Pedia : foot (athelte’s foot) Grey – infection Tinea Capites: head Yellow – jaundice , carotinemia Tinea Cruris: singit Pale – anemia Tinea Corporalis – body Representative Problems of the Skin: 1. Burn Trauma – injury to body tissue caused by excessive heat. INFANT 5-9 y/o ANTERIOR POSTERIOR Ant Post Head 9.5 9.5 6.5 6.5 Neck 1 1 1 1 Upper arm 2 2 2 2 Lower arm 1.5 1.5 1.5 1.5 Hand 13 1.25 1.25 1.25 Trunk 13 13 Back 13 13

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Genital @ buttocks Thigh Leg foot DEPTH: 1st degree – 2nd degree – 3rd degree –

1 2.5@ 2.75 2.5 1.75

2.75 2.5 1.75

1 2.5 @ 4 3 1.75

4 3 1.75

Partial thickness – superficial epidermis - erythema, dryness, PAIN Ex. Sunburn, heals by regeneration from 1 – 10 days Epidermis & portion of dermis- erythema, blisters, moist, extremely painful  scalds Full thickness- All skin layers: epidermis, dermis, adipose tissue, fascia, muscle & bone  lethargy, white or black, not painful – nerve endings destroyed  ex. lava burns

Mgt: Emergency: Prioritization depend on area of burn *1.) 1st aid

a.) Put out flames by rolling child on blanket b.) Immerse burned part on cold H2o *c.) Remove burned clothing of with sterile material, if none in the hosp. only d.) Cover burn with sterile dressing

2.) A/W a.) Suction PRN, o2 with increased humidity b.) Endotracheal intubation c.) Tracheostomy 3.) Prevention of shock & F&E imbalance : Burns: Hyperkalemia—MD will give insulin— for K to go back to cells a. colloids to expand blood volume b. isotonic saline to replace electrolytes c. dextrose & H2o to provide calories 4.) Tetanus Toxoid Booster 5.) Relief of pain – IV analgesic MORPHINE SO4 – needed for 2nd degree – very painful 6.) 1st defense of body – intact skin Prevention of Wound infection i. Cleaning & debriding of wound ii. Open or close method of wound care iii. Whirlpool therapy – drum with solution 7.) Skin grafting – 3rd degree – thigh or buttocks (autograft), pigs/ animals – xenograft frozen cadaver – hallow graft 8.) Diet – increase CHON, increase calories. 2. ATOPIC DERMATITIS - Infantile eczema (hika ng balat) (asthma of the skin) Papillovesicular erythematus lesions with weeping & crusting Usual Cause : Food allergies: milk, citrus juice, eggs, tomatoes, wheat Sx: > Extreme pruritus---linear excoriation----weeping crusting----- scaly shiny & white to ------------Lichenification Goal of Care:

1. Decrease pruritus – avoid food allergen 2. Diet: Prosobi or Isomil 3. Hydrate skin w/ burrow solution 4. Topical Steroids ---1% hydrocortisone cream 5. Prevent infection – proper hand washing, trim nails/cut short

3. IMPETIGO- skin disease. Causative agent – Grp. A beta Hemolytic streptococcus (GABHS), possibly staphylococcus > Papulovesicular surrounded by localized erythema becomes purulent & oozes a honey colored crust 4. PEDICULOSISCAPITIS –“KUTO” Mgt: proper hygiene – wash soap and H2o, oral penicillin – bactroban ointment *Can lead to acute glomerulonephritis AGN ---common to children with this type

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5. ACNE- adolescent problem >Self limiting inflammatory disease – sebaceous gland *Comedones – sebum causing white heads *Sebum- lipids of cholesterol causing acne bulgaris Mgt: Proper hygiene- mild soap or sulfur soap- antibacterial retin A or tretinoi Liver clearance before using Retin a: C/I to pregnant women 6. ANEMIA -pallor Causes: 1.) Early cutting of cord – preterm – cut umbilical cord ASAP Full term – cut umbilical cord when pulsation stops 2.) Bleeding disorders – blood dyscrasias Ex. a. Hemophilia – deficiency of clotting factor. Pattern of Inheritance : X linked recessive Usual carrier : mother (with X chromosome carrying the disease) Usually affected children: Son If mom – carrier, son – affected If father carrier- transmitted to daughter 3 Types: Hemophilia A – Deficiency of coagulation component factor 8 (classic/most common) Hemophilia B –or Christmas disease, deficiency of clotting factor 9 Hemophilia C – deficiency of clotting factor 11 Assessment: >Omphalagia – earliest sign >30cc in newborn >Newborn receive maternal clotting factor –reason why late Dx of hemophilia >Newborn growing – sudden bruising on bump area- marks earliest sign >Continuous bleeding – Hemarthrosis >damage or repeated bleeding of synovial membrane Dx test : PTT = Partial thromboplastin time – reveals deficiency in clotting factor *Long Term Goal- prevention of injury Nsg Dx: Increase risk of injury HT: avoid contact sport, swimming only, don’t stop immunization – change gauge of needle Falls –1st splint then immobilized , elevate affected part, apply pressure-not more then 10 min Of cold compress to prevent necrosis > Determine case before doing invasive procedure > No Aspirin > BT : Fresh frozen plasma or cryoprecipitate > Long-Term Goal: Prevention of Injury 7. LEUKEMIA - group of malignant disease characterized by > Rapid proliferation of immature WBCs Ratio: 500 RBC:1 WBC > WBC – protection from infection, soldiers of body > Immature WBC takes the nutrients from mature WBC Classification : 1. Lympho – affects lymphatic system 2. Myelo – affects bone marrow 3. Acute / blastic- affects immature cells 4. Chronic/ cystic- affects mature cells Most common cancer = (ALL) Acute Lymphocytic Leukemia *Main cause of Anemia: Failure of bone marrow to produce RBC S & Sx: TRIAD 1. From invasion of bone marrow Signs of Infection: a. Fever b. Poor wound healing c. Bone weakness & causes fracture Signs of Bleeding : a.) Petecchiae-small, round, flat, dark red spot

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b.) Epistaxis c.) Blood in urine & emesis Signs of Anemia : a.) Pallor , body malaise , constipation 2. From invasion of body organ: a. Hepatosplenomegaly b. Abdominal pain c. CNS affectation & increase ICP Dx Tests: 1. 2. 3. 4.

5. 6.

PBS- peripheral blood smear – determine immature WBC CBC – determine anemia, leukocytosis, thrombocytopenia neutropenia >done weekly during maintenance phase of therapy Lumbar puncture (LP) – determine CNS involvement. Before LP, Fetal position Best: Avoid flexion of neck – will cause a/w obstruction.“C” position or shrimp. Bone marrow aspiration – determine blast cells or immature WBC > *Common site for BMA = Iliac crest > Post BMA s/effect – bleeding apply pressure. Put pt on affected side to prevent hemorrhage Bone scan – determine bone involvement CT scan – determine organ involvement, CNS affectation

Therapeutic Mgt: TRIAD FOR CANCER: 1. 2. 3.

Surgery Irradiation Chemotherapy

Focus Nsg Care: Prevent infection 4 LEVELS OF CHEMOTHERAPHY---Goal of Tx: Achieve remission 1. Induction: every level is 1 session Meds: IV vincristine L- agpariginase Oral prednisone 2. Sanctuary- Treat leukemic cells that invaded testes & CNS *Give: Methotrixate- adm. intrathecally via CNS or spine cytocine, Arabinoside, steroids with irradiation 3. Maintenance- to continue remission Give: Oral Methotrisate – check WBC/ CBC order 1st before administering drug Adm. of methotrisate – do weekly WBC check 4. Reinduction – treat leukemic cells after relapse occurs. Meds – same as induction Give antigout agents: allopurinol or Zyloprim- treat or prevent hyperurecemic nephropathy. Nsg mgt:

Outstanding Nsg Dx:

1. High risk for infection 2. Alteration in nutrition less body requirement. 3. Alteration in Body image 4. Anticipatory grieving for family & parents Based on Maslow’s hierarchy

S/E of Chemotherapy 1. N/V – adm anti-emetic drugs 30 mins before chemo until 1 day after chemo 2. Ulcerations / stomatitis / abscess of oral mucosa: Nsng. Dx: Altered oral mucus membrane > Oral care – alcohol free mouthwash , betadine mouthwash > Don’t brush – use cotton pledgets > Topical xylocaine before meals > Diet- soft, bland diet according to child’s preference Temporary S/E of Chemo: Alopecia – altered body image Hirsutism – abnormal growth of hair to other body parts -give emotional support to parents, always repeat instructions Irradiation Management:

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3 principles:

1. Time 2. Distance 3. Shielding > with visitors but not more than 10 New Management: Chemotherapy or Bone Marrow Transplant 8. Hemolytic Disorders: a.

Hemolysis = destruction of RBC

Rh Incompatibility > “Rhesus” means foreign body > mother (-), fetus & father (+) > 4th baby severely affected > if (-) or no antigen : CHON factor > (+) has antigen : CHON factor

Erythroblastosis Fetalis = hemolysis or destruction of RBC d/t

O2 carrying capacity

S & Sx: Intrauterine growth retardation w/ pathologic jaundice w/in 24 hrs. b. ABO Incompatibility Most common incompatibility – ( mom) O – ( fetus) A Most severe incompatibility (Mom) O– (Fetus) B Assessment: Can affect 1st pregnancy RBC - 20 days lifespan O = universal donor AB = universal recipient Dx: Coomb’s Test Indirect: mother ----- normal result is (-) Direct : from baby---normal result is initially (-) Drug Of Choice: Rhogam Vaccine given to mothers (-) w/in 72 hrs. post-exposure to fetal RBC’s to destroy fetal RBC’s, then preventing Rh sensitization or antibody formation > given only w/in 72 hrs. once only 1st pregnancy 9. Hydrops (h20) Fetalis – edematous on lethal state with pathologic jaundice Within 24 h Mgt. for both: 1. Initiate feeding 2. Temporary suspension of breastfeeding to prevent kernicterus >content breast milk pregnanedioles – that delays action of glucoronyl transferase—a liver enzymes that converts indirect bilirubin to become direct bilirubin 3. Needs phototherapy 4. Needs exchange therapy 10. Hyperbilirubinemia - > 12 mg/dL of indirect bilirubin among full term *Normal Value: 0-3 mg/dL - bilirubin encephalopathy 11. Kernicterus - > 20 mg/dL among full term & >12 mg /dl of indirect for pre-term----lead to cerebral palsy *Physiologic Jaundice –(Icterus Neonatorum) jaundice within 48 -72 h (2-3 days)------ NORMAL -- just expose to morning sunlight *Pathologic Jaundice – (Icterus Gravis) jaundice w/n 24h or Jaundice during delivery d/t small Rh/edematous ABO *Breastfeeding Jaundice—caused by pregnanediole (6-7th day) Pathophysiology: ------------------- Destroyed RBCs releases Heme

Globin brokendown

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Iron (removed in the body) (not involved in jaundice)

Protoporphyrin broken down Indirect Bilirubin (fat-soluble converted by kidney) Converted by Glucoronyl Transferase (liver enzyme)

Direct Bilirubin (water-soluble) Assessment of Jaundice : *1. Blanching neonates forehead, nose or sternum (use 2 thumbs to separate skin folds) - yellow skin & sclerae - color of stool – light stool - color of urine – dark urine Mgt: Phototherapy or photo oxygenation (Normal HT: 18-20 inch.) Nsg Resp: 1. Cover eyes – prevent retinal damage 2. Cover genitals – prevent Priapism – a painful continuous erection 3. Change position regularly – even exposure to light 4. Increase fluid intake – prone to dehydration 5. Monitor I&O – weigh baby diaper – 1 g= 1cc 6. Monitor V/S – avoid use of oil or lotion due- heat at phototherapy > Bronze baby syndrome------transient S/E of phototherapy

4. Head – largest part of baby , ¼ of its length Normal head : 33-35 cm or 13-14 inches Size: Anterior Fontanel 1 x 1 Posterior Fontanel 3 x 4 A. Cephalo-caudal Assessment: Noticeable Structures of the Head: 1.

Craniostenosis or Craniosyntosis – premature closing of anterior fontanel

2. Microcephaly – small, slow growing brain d/t alcohol & HIV mom >5th percentile 3. Anencephaly – absence of cerebral hemisphere 4. Craniotabes – localized softening of cranial bone. Common – 1st born child (normal) -d/t early lightening (2 weeks prior to EDD) Rickets’ d/t Vit. B deficiency – soft cranial bone in older children 5. Caput Succedaneum – edema of scalp d/t prolonged pressure at birth Characteristics: 1. Present at birth 2. Crosses suture lines 3. Disappear after 2-3 days 6. Cephalhematoma- collection of blood due to rapture of periosteal capillaries Characteristics : 1. Present after 24 hours 2. Never cross suture line 3. Disappear after 4-6 weeks 4. Monitor for developing jaundice

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7. Seborrheic Dermatitis – ‘Cradle Cap” Scaling, greasy appearing salmon colored patches – seen on scalp behind ears and umbilicus Cause: - improper hygiene Mgt: 1. Proper hygiene 2. Put oil night before shampoo (use baby oil or virgin oil) 3. Use of fine-toothed comb 8. Hydrocephalus – excessive accumulation of CSF d/t anterior fontanel open after 18 months 2 Types: 1. 2.

Communicating – extra ventricular hydrocephalus Non-communicatinga. Intraventricular hydrocephalus b. Obstructive hydrocephalus d/t tumor obstruction Nsg. Dx: High Risk For Injury Dx For Seizure Activity : EEG

Sx: a. Abnormally large head, bulging fontanel –Earliest Sx of ICP b. Cushing’s Triad----- Hyper, bradypnea,bradycardia c. High pitched cry d. For older children & >6 months – Diplopia – eye deviation, projectile vomiting---earliest sx e. Fontanel bossing – prominent forehead f. Prominent skull vein g. Sunset eyes Mgt: a. Position to lessen ICP – low semi-fowlers 20-30 degree angle b. Administer- osmotic diuretic Mannitol/ Osmitrol , Diamex- Azetam c. Decrease CSF production ----drug: acetazolamide or Diamox d. Shunting – AV shunt or Vp shunt (ventriculoperitoneal shunt) Shave hair – in OR – to prevent growth of micro org. e. Hyperventilate child Nsg Care: 1.) Post VP shunt –position: immediately after---supine then after anesthesia --- side lying on non operated site - to prevent increase ICP Monitor for good drainage in catheter: good sign is a sunken fontanel if bulging fontanel – blocked shunt Catheter change as child is growing

5. Senses A. Assessment of Eyes:

1. Check for symmetry 2. Sclera – normal color – light blue then become dirty white 3. Pupil – round- adult size 4. Cornea – round & adult size * If large – Congenital Glaucoma NOTE FOR: *Coloboma- part of iris is missing (notching)

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Sign: Key hole pupil *Brushfields Spots -----iris black with white spots *Congenital Cataract-----Whiteness & Opacity of lens

COMMON TESTS Age

Common Tests

1. Newborn General Appearance:  Can only see 10-12 inches  Visual Acuity 20 /200 to 20/ 800

*DOLL’S EYES TEST------ Test for blindness = Done on the 10th day = Pupil go to opposite direction when head is moved *GLOBELLAR’S TEST -------Test for Blink Reflex. = Points near nose & the baby should blink

Infant & Children

* Test the ability to follow object past midline

2. 3 years old to School Age

*ALLEN CARDS -----------Test for Visual Acuity = Show common pictures 20 ft away *ISHIHARAS PLATES = Test for Color Blindness

3. Preschool

*E CHART ------ Test for Stereopsi of depth perception * COVER TESTING TEST ----- Test for Strabismus = Cover 1 eye for 10- 15 minutes. Then remove. Note For: ESOTROPIA = inward movement of eye ball EXOTROPIA = outward movement of eye

4. School Age To Adult

* SNELLENS TEST ------- Test for normal vision * E CHART DISEASES:

1. RETINOBLASTOMA Outstanding Sign:

= Malignant tumor of the retina Cat’s Eye Reflex – the whitish glow of pupil - With red painful eye - Can lead to blindness

Mgt. a. Surgery: Enucliation – the removal of the eyeball & replacement of artificial aye B. Assessment of the NOSE  1. 2. 3. 4.

(Sense Of Smell)

Normal color of nasal membrane: Pinkish

Check for presence of creases & pale color of nasal membrane  Indicative of Chronic Rhinitis Check if inflamed & reddened  Indicative of infection Check for Flaring of Alenase  A case of RDS Check for Cyanosis at rest

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

Indicative of CHOANAL ATRESIA = The posterior nares obstructed with bone or membrane Sx:

a. Resistance during catheter insertion in suctioning b. Emergency---- Surgery within 24 hrs 5. Check for sense of smell = Blindfold the child & let him common foods 5.

Check for presence of hair in nose: Cilia  Adolescent with no hair with ulceration of nasal mucosa: Cocaine user NOTE FOR: a. EPISTAXIS or Nosebleed N.I: Position: Sit upright, head slightly forward to facilitate drainage & prevent aspiration Put Cold compress & apply gentle pressure Give Epinephrine *Most developed sense of newborn – SENSE OF TOUCH The way the baby can identify the mother C. Assessment of the Ears: (Sense of hearing) *1st sense to develop & last to disappear – HEARING * Normal Color of the Tympanic Membrane : Pearly Gray 1. Check for symmetry 

If ears not properly aligned with the outer cantus of eyes or low set ears: Suspect A. KIDNEY MALFORMATION: 1.

RENAL AGINESIS = the absence of kidney 2 Types: a. Unilateral = only 1 is present b. Bilateral = absence of 2 kidneys Sign in uterus : Oligohydramnios Sign in newborn: 2 vessel cord Sx: Failure to void within 24 hrs Mgt:

Kidney Transplant

2. PRUNE BELLY SYNDROME The newborn has a wrinkled abdomen that looks like a prune d/t abdomen swelled with fluid in the womb, then lost that fluid after birth, leading to puckering of excess skin. B. CHROMOSOMAL ABERRATIONS: Cause: Advance maternal age >35 y/o 1.NONDISJUNCTION = Uneven division of chromosome a. TRISOMY 21 or “DOWN SYNDROME” = Extra #21 chromosome = Related to advance paternal age: 47xx + 21 Sx: Low set ears Mongolian slant Broad, flat nose

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Epicanthal Fold = extra fold of eyelids Brushfield’s Spot = black & white specks in the iris Pectum Excavatum = sunken sternum Puppy’s neck Hypotonic = muscle tone prone to URTI Simian crease = a single transverse line on palm. Alert: Always check PR for tachycardia d/t hypotonia Check for respiration Check for mental retardation----educable b. TRISOMY 18 or “ENDVARD SYNDROME”

- Affecting more girls than three times as boys. - Caused by the presence of an extra number 18 chromosome Sx: Pecan Carinatum (protruding sternum) Small Jaw (micrognathia) Hypoplastic (underdeveloped) fingernails c. TRISOMY 13 “ PATAU SYNDROME” - Associated w/ multiple abnormalities, including defects of the brain that lead to seizures, apnea, deafness, and eye abnormalities. Sx: Coloboma Cleft lip & cleft palate Low set ears d. TURNER’S

“Monosomy X Syndrome/Bonnevie-Ullrich Syndrome” - Occurs only in females - The girl's cells are missing an X chromosome, or part of an X chromosome. Sx evident during puberty

Sx: Short height Lack of developing ovaries Sterile e. KLINEFELTER’S SYNDROME - 47XXY or XXY syndrome is a condition caused by a chromosome nondisjunction in males; affected individuals have a pair of X sex chromosomes instead of just one - Has male genitalia - No deepening of voice - Small testes, penis -sterile *Klinefelter – Calvin Kline – male

*Turner – Tina Turner – female

2. DELETION ABNORMALITIES = deletion of the genes on chromosomes a. CRI-DU-CHAT SYNDROME or “Chromosome 5p deletion syndrome” - Results from a missing piece of chromosome # 5. Sx: Severe mental retardation – outstanding sx Wide-set eyes (hypertelorism) Downward slant of the eyes (palpebral fissures) All other sx of down syndrome b. FRAGILE X SYNDROME or “Marker X Syndrome”

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- Changes in the long arm of the X chromosome - Most common cause of inherited mental retardation in males - A fragile area on the X chromosome (called FMR1) has repeats in the genetic code. The more repeats, the more likely there is to be a problem. Boys and girls can both be affected, but because boys have only one X chromosome, a single fragile X is likely to affect them more severely. Sx:

Same with other chromosomal abnormalities

3. TRANSLOCATION ABNORMALITIES - Abnormalities in chromosome structure follow a chromosome break & during the repair process, the reunion of the wrong segments of the chromosome. - Involves two nonhomologous chromosomes (e.g., chromosome 2 and chromosome 6). Following a break in each of the chromosomes & subsequent reunion, a segment of chromosome 2 becomes attached to chromosome 6 and vice versa. a. BALANCED TRANSLOCATION CARRIER - When there is no loss or gain of chromosomal material & the individual is mentally & physically normal. However, there is an increased risk of having chromosomally abnormal offspring because individuals who carry balanced chromosome rearrangements may produce chromosomally unbalanced gametes. b. UNBALANCED TRANSLOCATION SYNDROME - Happens if following repair, there is a loss or gain of chromosomal material . There are significant clinical consequences for this type. 4. Others a. MOSAICISM – a situation where the nondisjunction of chromosomes occurs during the mitotic cell division after fertilization results to diff. cells contains different # of chromosomes. - Where an individual has two or more cell populations that differ in genetic makeup. This situation can affect any type of cell, including blood cells, gametes (egg and sperm cells) & skin. b. ISOCHROMOSOMES – a situation w/in the chromosomes instead of dividing vertically it divides horizontally NOTE FOR: *OTITIS MEDIA = Inflammation of middle ear Common to children d/t wider & shorter Eustachian tube Causes : 1. Bottle propping w/c may also lead to dental carries 2. Cleft lip/ cleft palate Sx:

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During Otoscopic Exam: Bulging tympanic membrane Absence of light reflex Observe for passage of milky, purulent foul smelling odor discharge Observe for URTI

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Nsg Care:

1. Position: Side-lying on affected aside – to facilitate drainage 2. Supportive Care- Bed rest, increase fluid intake Med Mgt: 1. Massive dosage antibiotic to prevent complication of Bacterial Meningitis 2. Apply ear ointment 3. Mucolytics How? School age : Pull pinna up & down < 3 y/o = down & back > 3 y/o = up & back Small child = down & back ( no age) 4. Surgery : Myringotomy w/ Tympanostomy Tube Insertion: Prevents permanent hearing loss Nsg. Care: Post surgery: Position on affected side for drainage When taking a bath put ear plugs on both ears If tympanous tube falls – healed already- usually 6 months D. Assessment of the Mouth & Tongue 1. Check for Symmetry NOTE FOR: a. BELL’S PALSY: - Facial nerve injury to the Cranial Nerve #7 w/c causes paralysis d/t forcep delivery Sx: 1.

Continuous drooling of saliva *Drooling Indicates 2 disorder:

2. Mgt:

Bell’s Palsy & TEF/TEA

Inability to open the eye & close the other eye at the same time---monitor for dryness

Refer to PT

b. TRACHEOESOPHAGEAL FISTULA/ATRESIA ( TEF /TEA) - TEF – there is a thin connection bet. the esophagus & stomach - TEA – there is no connection bet. the esophagus & stomach

C

Outstanding Sx: 4 C’s

Mgt:

Coughing Choking Continuous drooling Cyanosis

Emergency surgery

c. EPSTEIN PEARL : - White glistering cyst at palate & gums r/t hypercalcemia ( 1-2 small shiny mass) d. NATAL TOOTH - Tooth at birth d/t Hypervitaminosis of mother during pregnancy - If movable remove with a clean gauze

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f. NEONATAL TOOTH - Appearance of temporary teeth w/n the 28 days of life instead of 6 months * ANODONTIA – No eruption of temporary teeth even at 5 y/o g. ORAL MONILIASIS or ORAL THRUSH “Oral Candidiasis” - White cheese-like substances & curd like patches that coats tongue CA: Candida Albicans Nsg Care: Do not remove, wash mouth with cold boiled water Administer meds: Nystatin / Mycostatin: Antifungal g. *KAWASAKI DISEASE or “Mucocutaneous Lymphnode Syndrome” - A Strawberry tongue, originated in Korea - Dr. Kawasaki discovered it - Common in Japan Criteria For Diagnosis Of Kawasaki Disease 1. Fever lasting more than 5 days 2. Bilateral Conjunctivitis 3. Changes of lips & oral cavity - Dry, red fissure of lips - Strawberry tongue - Diffuse erythema of hands & feet 4. Changes of Peripheral Extremities - Erythema of the hands & soles - Indurative edema of the hands & feet - Membranous desquamation from fingertips 5. Polymorphous rash 6. Acute nonpurulent swelling of cervical lymph node to > 1.5 cm in diameter Complication: Myocardial Infarction in Children ( only MI in children) Mgt:

Administer Drug: Aspirin Gamma Globulin

E. Assessment of the Lips 1. Check for symmetry NOTE FOR: a. *CLEFT LIP - Failure of median maxillary nasal processes to fuse by 5-8 wks of pregnancy - Common to boys - Unilateral b. *CLEFT PALATE - Failed palate to fuse by 9 – 12 wks of pregnancy - Common to girls - Unilateral or bilateral Sx: 1. Evident at birth 2. Milk escapes to nostril during feeding 3. Frequent colic & otitis media or URTI Nsg Care: 1. Provide soft & large nipples---cross cut 2. Burp baby often

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Mgt: 1. Surgery : Depends on the Rule of 10 10 wks. Old 10 grams HgB 10 lbs. weight a. Cleft Lip Repair = Cheiloplasty - Done 1-3 months to save sucking reflex (lost in 6 months ) b. Cleft Palate Repair = Uranoplasty - Done 4-6 months to save speech Pre- Operative Care: 1. Provide emotional support especially to mom 2. Provide Proper nutrition to prevent colic Feeding : Upright seating position Burp frequently : 2x at middle & after feeding in a prone position& in a lower to upper tap 3. Orient parents to type of feeding Rubber tipped syringe = Post-cheiloplasty Paper cup/ soup spoon/ plastic cup = Post-uranoplasty 4. Apply restraints; Elbow restraints pre-opt so baby can adjust post op & decrease movement 5. 7-8 years after: Velopharyngeal Flap Operation: To fix nostril & pharynx  ALL Operation for mouth (adenoidectomy, tonsillectomy): MOST IMPORTANT DIAGNOSTIC TEST TO CHECK: CLOTTING TIME



Condition that warrants suspension of operation: COLDS & PHARYNGITIS = can lead to generalized infection TO SEPTICEMIA

Post Operative Nsg Care: 1. Airway: Position post-cheilopasty : Side lying to facilitate drainage Post-uranoplasty (tonsillectomy): Prone position to increase mucus secretion Avoid using straw,spoon,fork 2. Assess for RDS & signs of bleeding 3. Assess for bleeding: Frequent swallowing 6-7 days after surgery indicates bleeding 4. Proper nutrition Post-NPO: Children- offer first sterile water before clear liquid Clear liquids: Gelatin except red or brown color it may mask bleeding (Popsicle- not ice cream) Full liquid Soft diet Regular diet 5. Maintain integrity of suture line such as: Logan bar – wash ½ strength Hydrogen Peroxide & saline solution: Bubbling effect traps microorganism Prevent crusting & scarring by putting sterile gauze + NSS - Prevent baby form crying give analgesic for pain 6. Assessment of the Neck 1. Check for symmetry NOTE FOR: a. CONGENITAL TORTICOLIS or “ Wryneck”

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- Congenital shortening or Birth injury of sternocleidomastoid muscle during delivery d/t excessive traction at cephalic delivery Mgt: Daily passive stretching exercise Surgery Complication : Scoliosis 2. Check the thyroid gland – for basal metabolism

b. CONGENITAL CRETINISM - Absence or non functioning thyroid glands or Hypothyroidism Reasons for Delayed Dx: 1. 2. 3.

Thyroid glands covered by sternocleidomastoid muscles in newborn Baby received maternal thyroxin Baby sleeps 16 – 20 hrs a day Earliest Sign: 1. 2. 3. 4. 5. Late Sign:

Change in Sucking -1st Change in Crying – 2nd –decrease sound Sleep excessively Constipation d/t decrease peristalsis Edema – moon face

1. Mental Retardation Prognosis: Mental retardation preventable when Dx is early New Born Screening: it is included in the 6 diseases to be tested Dx: 1. 2. 3.

PBI- Protein Bound Iodine RIA - Radioimmunoassay Test Radioactive Iodine Uptake

Mgt: Synthroid (Sodium Levothyrosin) = Synthetic thyroid given lifetime Check PR before giving synthroid Tachycardia = Sx of Hyperthyroidism 7. Assessment of the Chest 1. Check for Symmetry NOTE FOR: a. WITCH MILK - Transparent fluid coming out from newborn r/t hormonal changes b. Respiratory Distress Syndrome (RDS) - Retroactive chest c. PECTUS EXCAVATUM - Sunken Sternum d. BRONCHCOLITIS - Distention of the alveoli - Viral in origin Sx: - Respiratory Distress - Increase RR > 60/minute - Wheezing: high-pitch on expiration

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8. Assessment of the Abdomen 1. Assess in order:

a. b. c. d.

Inspection Auscultation Percussion Palpation

I A P P =Last to perform because it will change bowel sounds

*Normal contour of the abdomen = Slightly protruding NOTE FOR: a. DIAPHRAGMATIC HERNIA - Sunken abdomen or the protrusion of stomach content thru a defective diaphragm d/t failure of pleuroperitoneal canal to close (located at the left postero-lateral side) Sx: 1. 2. 3.

Sunken abdomen Signs of RDS R to L shunting

Mgt: 1. Emergency surgery within 24h Diaphragmatic Repair w/ the use of Teflon Patch while place on (ECMO) Extra Corporal Membrane Oxygenation 2. Continuous CPAP & CPPB b. OMPHALOCELE – Protrusion of stomach contents in bet. junction of abdominal wall & umbilicus. Mgt: Very small surgery – return the stomach contents If large: Suspension surgery - Let the baby grow more to accommodate the stomach content Nsg Mgt: 1. Protect the sac with sterile wet dressing 2. Apply silver sulfadiazine ointment to prevent infection c. GASTROCHISIS - Absence of the abdominal wall exposing all the stomach contents Nsg Mgt: 1. Provide sterile wet dressing 2. FUNCTION OF THE GIT a. b. c.

Assists in maintaining F&E & acid base balance Processes & absorbs nutrients to maintain metabolism & support G & D Excrete waste products from digestive process

Newborn:

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Gastric Capacity – 1-2 oz Gastric Emptying – every 2-3 hrs. Normal Body Weight – 3,000 to 3,500 grams

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3. RECOMMENDED DAILY ALLOWANCE Calories : 120 cal / Kbw/day or 360 – 380 cal/ day CHON = 2.2g /Kbw/day Fluids = 16-20 cc/kg/day 4. PRINCIPLES IN SUPPLEMENTARY FEEDING *Supplementary Feeding usually at 6 months *Supplementary feeding can be given as early as 4 months *Weaning starts at 6-9 months or when shortening the nursing time *Never wean a child when in crisis a.) Solid food offered to baby in the ff. sequence! 1st - Cereals – rich in iron—Reserves is catabolized already by 6 months 2nd - Fruits 3rd - Vegetables 4th - Meat b.) Begin with small quantities c.) Finger foods – offered 6 months d.) Soft table food – “modified family menu” given by 1 year e.) Dilute fruit juices & offered by 6 months Ratio of fruits to water 1:4 (1 squeeze orange = 1 ounce) f.) Never give half cooked eggs – usually causes of Salmonellosis/Gastroenteritis g.) Don’t give honey may cause Infant Botulism h.) Offer new food one at a time – interval of 4 – 7days or 1 week To determine food allergens 5. MAJOR CONCEPTS OF FLUID & ELECTROLYTE BALANCE Total Body Fluids: Comprises 65 - 85% of body wt of infants & children Where fluids are greater in infants: ECF – reason why babies prone to develop dehydration 6. ACID BASE BALANCE Dependent on the ff: a. Chemical buffers b. Renal & Respiratory system involvement c. Dilution of strong acids & bases in blood IMBALANCE: a. RESPIRATORY ACIDOSIS = Carbonic acid excess Causes: Hypoventilation RDS COPD

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Laryngotracheobronchitis (LTB) b. RESPIRATORY ALKALOSIS = Carbonic acid deficit Causes: Hyperventilation Fever Encephalopathy c. METABOLIC ACIDOSIS = Base HCO3 deficit Causes: Diarrhea Severe dehydration Malnutrition Celiac crisis d. METABOLIC ALKALOSIS = Base HCO3 excess Alkalosis Up Causes: Uncontrolled vomiting NGT aspiration Gastric lavage 7. CONDITIONS THAT PRODUCES F & E IMBALANCE

Acidosis Down

a. VOMITING = Forceful expulsion of stomach content Sx:

1. 2. 3. 4.

Nausea Dizziness Facial flushing Abdominal cramping

Assessment: Mgt:

Amount, Frequent & force Projectile Vomiting – Indicates Increase ICP or Pyloric Stenosis BRAT DIET B – banana R – rice A- apple sauce T- toast

b. DIARRHEA – Exaggerated excretion of intestinal contents Types: 1. ACUTE DIARRHEA/ INFECTIOUS - Associated with the ff: a. Gastroenteritis b. Salmonellosis c. Dietary indiscretions d. Antibiotic use (Ampicillin, Tetracycline) CA:

Bacteria (salmonella, shigella) Virus (Rotavirus- most common) Prozoan (Entamoeba histolytica)

2. CHRONIC-NON SPECIFIC DIARRHEA/NON-INFECTIOUS Cause: a. Food intolerance b. Excessive fluid intake c. CHO, CHON malabsorption (abnormality) d. Allergy e. Irritable colon Assessment: Frequency, Consistency, Appearance of green colored stool Created by Niňa E. Tubio

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*Best criteria to determine diarrhea : Consistency Complication: 1. DEHYDRATION Mild dehydration Moderate dehydration Severe dehydration

Early Signs

5% wt loss 10% wt loss 15 % wt loss

Signs of Dehydration Hypotension Tachycardia ---- 1st sign in newborn Tachypnea + Fever Weight loss -----Best criteria to determine dehydration Sunken fontanel & eyeballs Scanty & dark urine Absence of tears Poor skin turgor Severe dehydration: Marked Oliguria & Prolonged capillary refill time > 3 sec.

Mgt: 1. Acute Diarrhea = NPO (to rest the bowel ) With fluid replacement – IV Oresol : 1 glass & 1 tsp. of sugar, 1 pinch of salt Prone to Hypokalemia : Give K chloride Before administering of K chloride : Check if baby can void If cannot void = Hyperkalemia Drug: Na HCO3 : Administer slowly to prevent cardiac overload 8. GASTRIC MOTILITY DISORDER: (Lower GIT Obstruction) a. HIRSCHPRUNGS DISEASE - Congenital aganglionic megacolon - Aganglionic: Absence of ganglion cells needed for peristalsis Earliest Sign in Neonate: 1. Failure/Delayed passage of mecomium after 24h 2. Abdominal distension 3. Vomitus of fecal material ---lead to aspiration----Atelectasis 4. Foul-smelling breath Signs in Early Childhood: 1. Ribbon like stool 2. Foul smelling stool 3. Constipations 4. Diarrhea Dx: 1. 2. 3. 4.

Barium Enema – Reveals narrowed portion of bowel Rectal Biopsy – Reveals absence of ganglionic cells Abdominal X-ray – Reveals dilated loops on intestine Rectal manometry – Reveals failure of intestine sphincter to relax

Therapeutic Mgt/Nsg care 1. NGT feeding: Measure tube from nose to ear to midline of xyphoid & umbilicus 2. Surgery a.) Temporary colostomy b. Anastomosis & pull through procedure Pre-opt: Provide Enema everyday

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Use NSS: Isotonic ( 1 tsp. sugar + 500 cc of H20) Not tap water: Hypotonic Can be absorbed by the cells----Circulatory Overload 3. Diet: Increase CHON Increase calories Decrease residue Ex. Offer pasta, spaghetti, chicken No corn, raisins ---may lead to aspiration b. GASTROESOPHAGEAL REFLUX (GER) or CHALASIA - Presence of stomach contents in the esophagus Assessment : 1. 2.

Chronic vomiting Failure to Thrive Syndrome 2 Types: a. Organic - d/t abnormality in the body/affected organ b. Non-organic – d/t abuse Esophageal bleeding manifested by Melena or Hematemesis

3. Complication: 1. Aspiration pneumonia 2. Esophagitis 3. Inflammation 4. Esophageal cancer (Organic type) Dx Procedure: 1. Barium Esophogram – reveals reflux 2. Esophageal Manometry – reveals lower esophageal sphincter pressure 3. Intraesophageal pH content – reveals pH of distal esophagus. Medication For GERD 1. Anti-cholinergic

a.) Betanicole (Urecholine) – To increase esophageal tone & peristaltic activity b.) Metachloporomide (Reglam) – To decrease esophageal pressure by relaxing pyloric & duodenal segments Increase peristalsis w/o stimulating secretions c.) H2 Histamine Receptor Antagonist – To decrease gastric acidity & pepsin secretion Ex. Zimetidine, Ranitidine (Zantac) – take 30 min before meals d.) Antacid – To neutralizes gastric acid between feedings. Ex. Maalox Surgery:

Nissen Funduplication - Creation of a valve mechanism by wrapping the greater curvature of the stomach

Nsg Care:

For Chronic vomiting: 1. Thickened feeding with baby cereals to prevent vomiting - effective if without vomiting 2. Feed slowly, burp often every 1 ounce 3. Positioning: < 9 months – supine on infant seat > 9 months – prone w/ head of mattress slightly elevated 30 degree angle

9. OBSTRUCTIVE DISORDERS a. PYLORIC STENOSIS – Hypertrophy of the muscles of pylorus causing narrowing & obstruction - Progressive thickening of the muscular layer of the pylorus

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Assessment: 1.) Outstanding Sx: Projectile vomiting d/t pressure from narrowed pylorus Nursing Alerts: a. Vomiting is an Initial Sign of Upper GI obstruction b. Vomitus of upper GI can be blood tinged not bile streaked. (with blood) c. Vomitus of lower GI is bilous ( with pupu) d. Projectile vomiting – increase ICP or GI obstruction e. Abdominal distension – Major Sign of Lower GIT Obstruction 2.) Metabolic Alkalosis 3.) Failure to gain weight 4.) Olive shaped mass – On palpation (almond-shaped mass) 5.) Peristaltic wave visible from L to R across epigastrum 6.) Always hungry, irritable Dx: 1. Ultrasound 2. X-ray of upper abdomen with barium swallow reveals a “STRING SIGN” Mgt: 1. 2.

Pyloromyotomy - incision of the pyloric muscle Fredret-Ramstedt Procedure – separation of hypertrophied muscle w/o incision

Nsg Care: 1. Serum electrolyte: Increase Na & K, Decrease chloride 2. If on enteral feeding, provide pacifier Pre-Opt: Post-Opt:

Thickened feedings (regular formula + Cereal) Monitor feedings (Clear liquid 24 hrs.) (Diluted Formula)

b. INSTUSSUSCEPTION - Invagination or telescoping of position of bowel to another - Common Site: Ilio-Cecal junction (Junction bet. the small intestine) Cecum is bigger than the ileum - Not congenital Prone People:

Person who eats too fast Too much activities involving the movement of the stomach

Complication:

Invagination O2 supply Necrosis Swelling-----burst -------Peritonitis: An emergency

Sx:

1.) 2.) 3.) 4.)

Persistent paroxysmal abdominal pain Vomiting Currant Jelly Stool: d/t bleeding & inflammation Palpable sausage shaped mass

Dx: 1.) X-ray with Barium Enema – reveals “Staircase Sign” (coiled spring) Mgt: 1.) Hydrostatic Reduction with barium enema 2.) Anastomosis & pull thru procedure 10. INBORN ERRORS OF METABOLISM Created by Niňa E. Tubio

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- Due to deficient liver enzymes a. PHENYLKETONURIA (PKU) - Genetic disorder that is characterized by an inability of the body to utilize the essential amino acid, phenylalanine d/t deficiency of liver enzymes (PHT) Phenylalaninehydroxylase Transferase : The liver enzyme that converts Phenylalanine to tyroxine or CHON to amino acid 9 Amino Acids: 1. Valine 2. Isolensine 3. Tryptophase 4. Lysine 5. Phenylalanine 6. Thyronine: Decrease melanin production Sx: a. Fair complexion b. Blond hair c. Blue eyes 7. Thyroxin: – decrease basal metabolism -Accumulation of Phenyl Pyruvic acid leads to: a. Atopic dermatitis b. Musty / mousy odor urine c. Seizure: Mental retardation Dx: 1. GUTHRIE TEST: Use blood as specimen Preparation: Increase CHON intake - Test if CHON will convert to amino acid 2. Specimen urine mixed with pheric chloride - Presence of green spots at diaper a sign of PKU Nsg Care: 1. DIET: Low phenylalanine diet: Food C/I : Meats, chicken, milk, legumes, cheese, peanuts Give Lofenalac: Milk with synthetic protein b. GALACTOSEMIA - Deficiency of liver enzyme GUPT: Galactose Urovil Phosphatetranferase Converts galactose to phosphate tranferase glucose Galactose will destroy brain cells if untreated – death within 3 days Dx: 1. Beutler Test = Get blood after 1st feeding Presence of glucose in blood: Sign of galactosemia Nsg Care: 1. Diet: Galactose free diet for lifetime 2. Give Neutramigen : Milk formula c. CELIAC DISEASE - Gluten enteropathy Assessment: Early Sx:

a. Diarrhea: Failure to gain weight following diarrheal episodes b. Constipation c. Vomiting d. Abdominal Pain: Protuberant abdomen even if with muscle wasting e. Steatorrhea Late Sx:

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1. 2.

Behavioral changes: Irritability & Apathy Muscle wasting & loss of subcutaneous fats

Celiac Crisis: Exaggerated vomiting with bowel inflammation Dx:

1. Laboratory Studies : Stool analysis 2. Serum Antigliadin & Antireticulin Antibodies: Confirmatory Dx of the disease 3. Sweat Test Nsg Care: 1. Gluten-free diet for lifetime 2. All brow food not allowed: Intolerance Common Gluten food: B- barley R- rye O- oat W- wheat 3. Allowed to eat rice & corn Mgt: 1. Vitamin supplements 2. Mineral supplements 3. Steroids PATHOPHYSIOLOGY: Gluten – Glutamine (Normal Absorption)

Gliadin (Toxic to epithelial cells of villi of intestines: Effects is malabsorption syndrome)

Malabsorption

Fats

CHON & CHO peripheral edema & malnutrition

Vit. D /Calcium

Vit. K

Iron folic acid

Inadequate blood coagulation

Steatorrhea

Osteomalasia

Bleeding

Anemia

11. POISONING - Common in Toddlers: Poisoning - Common to Infants: Suffocation & falls Principles : 1. 2. 3.

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Determine the substance taken & Assess LOC Unless poison is corrosive, caustic (strong alkali such as lye) or a hydrocarbon, INDUCE VOMITING is the most effective way to remove poison. Give SYRUP OF PECAC: oral emetic to cause vomiting after drug overdose/poisoning

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4. 5. 6. 7. 8.

15 ml : Adolescent, school age & pre school 10 ml to infant UNIVERSAL ANTIDOTE: Charcoal, Milk Of Magnesia & Burned Toast Never administer the charcoal before syrup of pecac Antidote for Acetaminophen Poisoning: N – Acetylcyctein (Mucomyst) For Caustic poisoning like Muriatic Acid: Give vinegar to neutralize acid . Don’t vomit prepare tracheostomy set For Gas poisoning : Give mineral oil to coat the intestine & prevent absorption of gas---go to stool

a. LEAD POSIONING Physiology:

Accumulation Lead Destroy RBC functioning Hypochronic Microcytic Anemia Destroy kidney functioning Accumulation of Ammonia Encephalopathy Sx: 1. Beginning symptoms of lethargy 2. Impulsiveness & Learning difficulties 3. As Lead increases, severe encephalopathy with seizure & permanent mental retardation Dx: 1. 2. 3.

Blood smear Abdominal X-ray Long bones

Mgt:

1. Remove child from the source 2. If lead is > 20 ug/dL: Need Chelation Therapy : Binds with lead & excreted by kidney Ex. BAL (Dimercaprol) Ca EDTA ( Edetate Ca Disodium) A chelating agent must be administered in a large muscle group VIA DEEP IM Check urine specific gravity (Normal: 1.003-1.030) S/E: Nephrotoxic N.I: Warm compress post-chelation to relieve pain 9. Assessment of the Reproductive Organ NOTE FOR: a. ANOGENITAL 1. Female: a. PSEUDOMENSTRUATION: - Slight bleeding on vagina R/T hormonal changes b. RAPE/CHILD ABUSE or BATTERED CHILD SYNDROME - Tearing of fourchette with blood Rape: Report within 48 h to brgy. Captain R.A. 7610 – CHILD ABUSE LAW - Non-accidental injury Characteristics of Abusive Parents: 1. Experience of childhood abuse 2. Too concerned, too many questions Sx: 1. Wound in different stages of healing

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2. Identical marks of wounds 2. Male: Assessment: 1. Assess scrotum with warm hands & warm room 2. Baby should pee w/in 24 hrs. NOTE FOR: a. UNDESCENDED TESTES or “CRYPTORCHIDISM” - Common to preterm (descend in 7 months) Surgery: Orchidopexy Complication: Sterility 3. Check for the arch of urination b. EPISPADIAS - Urinary meatus located dorsal or above glans penis c. HYPOSPADIAS - Urinary meauts located ventral or below glans penis Hypospadias w/ Chordee: Fibrous band causing penis to curb downward Mgt: Surgery d. PHIMOSIS = A tight foreskin Mgt: Circumcision e. PARAPHIMOSIS = loosened foreskin f. BALANITIS = Infection of glands penis d/t smegma g. TESTICULAR TORSION = Twisted testicle h. HYDROCEL

= Fluid -filled scrotum Dx: Transillumination with use of flashlight - glowing sign

i. VARICOCELE = Enlarged vein of epididymis (Girls = Valvular varicosities) 10. Assessment of the Urinary Tract NOTE FOR: a. WILMS TUMOR or NEPHROBLASTOMA - A neoplasm of the kidneys that typically occurs in children. - Most common type of kidney tumor - It is more common among some siblings and twins, which suggests a possible genetic cause. Sx: - Absence of the iris (aniridia) - Hemihypertrophy (enlargement of one side of the body) Alert: - No palpation or percussion----metastasis may occur Mgt: - Triad Treatment of Cancer Renal Disorder

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Cause

Sx

Tx

NSG CARE

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b. NEPHROTIC SYNDROME

Infectious

c.

AGN (Acute Glomerulonephritis) 3

1. 2. 3. 4. 5. 6. 7.

Autoimmune Grp. A betahemolytic streptococcus Or GABHS

A’s:

AGN Autoimmune, Grp. A Betahemolytic St.

Before: Sore Throat *Impetigo

Anasarca: General edema Massive protenuria Microscopic or no hematuria

1. Prednisone 2. Diuretic (Furosemide)

Focus of Care: 1. Monitor edema Weigh daily

Serum CHON decreased

2. Diet:

Serum lipid increased

Moderate CHON Increase K- OJ, beef broth, banana Low Na Diet

Fatigue Normal to low BP

1. (PPP) Primary Peripheral Periobital Edema 2. Moderate protenuria 3. Gross Hematuria (Sign: Smokey urine) 4. Serum K increased 5. Fatigue 6. *Increase BP – Outstanding Sx

1. Anti-HPN drug (Hydralazine or Apresoline) 2. Iron supplements

1. Weigh daily 2. Monitor : BP V/S Neurologic status 3. Diet: Decrease K Decrease Na

Complication : 1. Hypertensive encephalopathy If HPN not treated 2. Anemia

11. Assessment of the BACK 1. Check for flatness & symmetry *Spina Bifida – From L5 to S1 NOTE FOR: a. OPEN NEURAL TUBE DEFECT - Decreased Folic Acid intake of mother & those during pregnancy undergoes steam bath/spa 2 Types: 1. SPINA BIFIDA OCCULTA - Failure of post laminae of vertebrae to fuse Sx: Dimpling of the back Abnormal tufts of hair 2. SPINA BIFIDA CYSTICA - Failure of post laminae of vertebrae to fuse with a sac Types: 1.* MENINGOCELE - Protrusion of CSF & Meninges - No alteration in function 2. MYELOMENINGOCELE - Protrusion of CSF & Meninges & Spinal Cord - Most dangerous type - On the back : under illumination shows a half glow 3. ENCEPHALOCELE

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- CNS complication : Hydrocephalus--Cranial meningocele or Myelomeningocele Most Common Problem : a. b. c.

Rupture of sac Prone position Sterile wet dressing

Most Common Complication: Infection 1. For Myelomeningocele : Genitourinary & Fecal Incontinence 2. Orthopedic complication: Paralysis of lower extremities Sx: a. Weakness, paralysis of lower extremities b. Cold to touch c. Ulceration d. Absence of spontaneous movement e. Bladder – dribbling of urine g. Bowel – no control Dx: 1. During pregnancy thru MAFEP Mgt: Surgery just to prevent infection, will not cure Pre-opt – Protect the sac, use sterile doughnut ring Post op – prone position Nsg Care: Always check diaper b. SCOLIOSIS - Lateral curvature of the spine - Common to adolescence 2 Types: 1. Structural – d/t Wry neck 2. Postural – d/t improper posture or heavy bags Sx: 1. 2. 3.

Uneven hemline Bend forward & 1 hip higher 1 shoulder blade more prominent than the other

Nsg care: 1. Conservative – Avoid obesity, exercise 2. Preventive – Milwaukee brace : Worn 23 h a day 3. Corrective surgery – Insert Harrington rod Post operative- How to move : Log Rolling- move client as 1 unit 12. Assessment of the EXTREMITIES: 1. Assess for the # of digits = 20 NOTE FOR: a. SYNDACTYLY b. POLYDACTYLY c. OLIDACTYLY

- Webbing of digits (ginger-like foot) - Extra digits - Lack of digits

d. AMELIA e. POCOMELIA

- Total absence of digits - Absence of distal part of extremities Both d/t use of anti-emetic in Pregnancy or Thalidomides

2. Assess for movement of extremities

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a. ERB-DUCHENNES’ PARALYSIS - Paralysis of the brachial plexus injury or brachial palsy - Birth injury d/t breech delivery & excessive lateral traction Sx: 1. Unable to abduct arms from shoulders/ Rotate arm externally or supinate forearm 2. Absence or asymmetrical Moro reflex Mgt: 1. Rotate arms from shoulders with elbow flexed 2. Passive ROM exercises b. CONGENITAL HIP DISLOCATION - Head of femur is outside the acetabulum Types:

1. Subluxated : Most common type 2. Dislocated Sx: 1. 2. 3. 4. 5.

Shortening of affected leg Asymmetrical gluteal fold Limited movement – earliest sx (+) Ortolanis sign – abnormal clicking sound during abduction (away) When able to walk – child limps – Late Sx: Trendelenburg Sign

Goal of Mgt: Facilitate abduction Mgt. 1. 2. 3. 4. 5.

Triple diaper Carry baby astride Frejka splint Pavlik harness Hip Spica Cast

c. TALIPES or “Clubfoot” Types:

a.) EQUINOS = Plantar flexion (horsefoot) b.) CALCANEUS = Dorsiflexion: Heel lower that foot/ Anterior portion of foot flexed towards anterior leg

c.) VARUS = Foot turns in d.) VALGUS = Foot turns out e.) EQUINOS VARUS = Most common (Combination) Assessment: 1.

Straighten legs & flexing them at midline position

Mgt: 1. Corrective Shoe- Dennis brown shoe, spica cast 2. Cast 13. OTHER TOPICS: A. CAST Function of CAST: 1. To immobilize 2. To maintain bone alignment 3. To prevent muscle spasm Equipments: 1. Stokinette

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2. Lead pencil to mark area to be amputated 3. Plaster of Paris Nsg Care To Patients with CAST: 1. Cold H20 will hasten setting process 2. Hot H20 will slow setting process 3. After cast application : How to move pt: -Use open palm not fingers- fingers will cause indention 4. Dry cast with natural air not blower 5. If Cast with bleeding - Mark with ball pen edge of blood to know if bleeding is on going 6. sign that cast is dry: Resonant sound, cast cold to touch 7. Do petaline: making rough surface of cast smooth 8. Priority check : Neurovascular check: C - circulation M - motion S - sensation 9. Assess for circulation impairment: B - blueness or coldness L - lack of peripheral pulses E - edema not corrected by elevation P – pain on casted area T – tingling sensation B. CRUTCHES Function: 1. To maintain balance 2. To support the weakened leg Principles In CRUTCHES: 1. Weight of body on palm! 2. Brachial Pulsing – if weight of body in axilla 3. Do palm exercise- squeeze ball 4. Measure Crutches: 2 inches across bar of axilla 6 inches in front of the big toe Different Crutch Gaits: 1. 2.

Swing Through Swing to No weight bearing are allowed into lower ext

3. Three point Gait - wt bearing is allowed in 1 ext 4. Four point gait 5. Two point Gait - Weight bearing allowed in 2 lower extremities Other Crutch-Maneuvering Techniques To sit down: 1. Grasp the crutches at the hand pieces for control 2. Bend forward slightly while assuming a sitting position 3. Place the affected leg forward to prevent weight-bearing and flexion To stand up:

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1. Move forward to the edge of the chair with the strong leg slightly under the seat 2. Place both crutches in the hand on the side of the affected extremity 3. Push down on the hand piece while raising the body to a standing position To Go Down Stairs: 1. Walk forward as far as possible on the step 2. Advance crutches to the lower step. The weaker leg is advanced first and then the stronger extremity shares the work of raising and lowering the body weight with the patient’s arms. To Go Up Stairs: 1. Advance the stronger leg first up to the next step. 2. Then advance the crutches and the weaker extremity. (Strong leg goes up first and comes down last.) A memory device for the patients is “up with the good, down with the bad.”

C. WALKER -Provides more support than a cane or crutches D. CANE - Used to help pt. walk with greater balance & support & to relieve the pressure on weight-bearing joints by redistributing the weight. - The cane is held in the hand opposite to the affected extremity Methods of Transferring The Patient from the bed to a wheelchair: I. Weight-bearing transfer from bed to chair. The patient stands up, pivots his back is opposite the new seat, and sits down. II. (Left) Non-weight-bearing transfer from chair to bed. (Right) With legs braced. III. (Left) Non-weight-bearing transfer, combined method. (Right) Non-weightbearing transfer, pull-up method E. TRACTION - Used to reduce dislocation & immobilize fractures Principles of TRACTION: 1. 2. 3. 4.

The client should be in dorsal or supine position For every traction there is always a counter traction Line of pull should be in line with deformity For traction to be effective, it must be continuous

Types: Straight Traction Skin Traction Bryant’s Traction Buck’s Extension Skeletal Traction Nursing Responsibilities: 1. 2. 3.

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Assess for circulation and neurologic impairment It can lead to hypertension Be careful in carrying out nursing functions by not moving the weights

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F. AUTOIMMUNE SYSTEM Types of Immunity: a.

IMMUNITY AGAINST: = Diphtheria, Pertussis, Tetanus, Polio & Measles last for 9-12 months in babies

b. PASSIVE NATURAL - Via placenta, breast milk c.

ACTIVE NATURAL - Acquired disease & produces memory cells

d. PASSIVE ARTIFICAL - Receives anti-serum with anti-bodies from host - Hep. B e.

ACTIVE ARTIFICIAL - Receives vaccine & produces memory cells - All EPI vaccines are active artificial EXCEPT HEP. B 12. NEUROMUSCULAR SYSTEM Reflexes A. BLINK REFLEX - Rapid eyelid closure when strong light is shown B. PALMAR GRASP REFLEX - With solid object, baby will grasp object - Cling to mother for safety - 6 weeks to 3 months to disappear C. STEP IN/WALK-IN REFLEX - Neonate placed on a vertical position with their feet touching a hard surface will take a few quick, alternating steps. * PACING REFLEX – Almost the same with step in place reflex only that you are touching the anterior surface of a newborn’s leg D. PLANTAR GRASP REFLEX – When an object touches the sole of a newborn’s foot at the base of the toes, the toes grasp in the same manner as the fingers do. E. TONIC-CLONIC REFLEX – When newborns lie on their backs, their heads usually turn to one side or the other. The arm on the leg on the side to which the head turns extend, and the opposite arm and leg contract. F. MORO REFLEX – Letter “C” position - Disappears 4-5 months - Test for neuro integrity

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G. MAGNET REFLEX – when there is pressure on the sole of the foot he pushes back against the pressure H. CROSSED EXTENSION REFLEX – When the sole of the foot is stimulated by a sharp object, it causes the foot to rise and the other foot extend I.

TRUNK INCURVATION REFLEX – While in prone position & the paravertical area is stimulated, it causes flexion of the trunk and swing his pelvis towards the touch

J.

LANDAU REFLEX – While in prone position and the trunk is supported, the baby exhibit some muscle tone

K. PARACHUTE REACTION – While on ventral suspension, with the sudden change of equilibrium, it causes extension of the hand and legs L. BABINSKI REFLEX –When the sole of the foot is stimulated by an inverted “J”, it causes fanning of the toes

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